Publications - Page 9 sur 57 - RespiFIL - Filière de santé des maladies respiratoires rares

Voici les publications scientifiques relatives aux maladies respiratoires rares auxquelles les membres de la filière ont contribué, classées par groupes de pathologies (depuis juillet 2021).

Maladies pulmonaires chroniques kystiques (LAM/MKPM)
Pulmonary Function Test Results Are Correlated with 6-Minute Walk Distance, Distance-Saturation Product, and 6-Minute Walk Work in Patients with Lymphangioleiomyomatosis

Diesler, Rémi, Vincent Cottin, Yves Gallien, Ségolène Turquier, Julie Traclet, Kais Ahmad, et Jean-Charles Glerant.

Respiratory Medicine and Research 85 (juin 2024): 101071.
Maladies pulmonaires chroniques kystiques (LAM/MKPM)
Characteristics and Outcomes of Patients with LAM Receiving Sirolimus in France Based on Real-Life Data

Cottin, Vincent, Antoine Cases, Virginie Bourdin, Martine Reynaud-Gaubert, Sandrine Hirschi, Mallorie Kerjouan, Rémi Diesler, et al.

Frontiers in Medicine 11 (janvier 2025).
Maladies pulmonaires chroniques kystiques (LAM/MKPM)
Description des caractéristiques et de l’évolution clinique de la lymphangioléiomyomatose (LAM) chez les patientes traitées par sirolimus en France

Cottin, V., L. Wemeau, B. Chardès, J. Rudant, V. Ellebode, S. Fievez, N. Assi, A. Schmidt, H. Denis, et Y. Uzunhan.

Revue des Maladies Respiratoires Actualités 16, nᵒ 1 (janvier 2024): 20‑21.
Hypertension pulmonaire (HTP)
Phenotypes in Pulmonary Hypertension

Weatherald, Jason, Anna R. Hemnes, Bradley A. Maron, Lisa M. Mielniczuk, Christian Gerges, Laura C. Price, Marius M. Hoeper, et Marc Humbert.

European Respiratory Journal 64, nᵒ 3 (septembre 2024).
Hypertension pulmonaire (HTP)
4D Flow Cardiac MRI to Assess Pulmonary Blood Flow in Patients with Pulmonary Arterial Hypertension Associated with Congenital Heart Disease

Valdeolmillos, Estibaliz, Hichem Sakhi, Marine Tortigue, Marion Audié, Marc-Antoine Isorni, Florence Lecerf, Olivier Sitbon, et al.

Diagnostic and Interventional Imaging 105, nᵒ 7‑8 (juillet 2024): 266‑72.
Hypertension pulmonaire (HTP)
Thirty Years of Surgical Management of Pediatric Pulmonary Hypertension: Mid-Term Outcomes Following Reverse Potts Shunt and Transplantation

Valdeolmillos, Estibaliz, Jérôme Le Pavec, Marion Audié, Laurent Savale, Xavier Jais, David Montani, Olivier Sitbon, et al.

The Journal of Thoracic and Cardiovascular Surgery 168, nᵒ 3 (septembre 2024): 943‑54.
Hypertension pulmonaire (HTP)
Percutaneous Atrial Septal Defect Closure in Patients with Pulmonary Arterial Hypertension

Valdeolmillos, Estibaliz, Claire Foray, Gregoire Albenque, Clément Batteux, Jerome Petit, Florence Lecerf, Xavier Jaïs, et al.

The European Respiratory Journal 63, nᵒ 5 (mai 2024): 2301649.
Hypertension pulmonaire (HTP)
Bioreactance Assessment of Cardiac Output Lacks Reliability for the Follow-up of Patients with Pulmonary Hypertension

Turquier, Ségolène, Laure Huot, Medhi Lamkhioued, Fabien Subtil, Julie Traclet, Kais Ahmad, François Lestelle, Louis Chauvelot, Vincent Cottin, et Jean-François Mornex.

PloS One 19, nᵒ 5 (mai 2024): e0298727.
Hypertension pulmonaire (HTP)
Deep Phenotyping of Unaffected Carriers of Pathogenic BMPR2 Variants Screened for Pulmonary Arterial Hypertension

Tóth, Eszter N., Lucas R. Celant, Marili Niglas, Samara Jansen, Jelco Tramper, Nicoleta Baxan, Ali Ashek, et al.

European Respiratory Journal 64, nᵒ 4 (octobre 2024).
Hypertension pulmonaire (HTP)
Pulmonary Hypertension Induced by Right Pulmonary Artery Occlusion: Hemodynamic Consequences of Bmpr2 Mutation

Todesco, Alban, Julien Grynblat, Kouamé Kan Firmin Akoumia, Damien Bonnet, Pedro Mendes-Ferreira, Stéphane Morisset, Denis Chemla, et al.

Journal of the American Heart Association 13, nᵒ 14 (juillet 2024): e034621.

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Pulmonary Function Test Results Are Correlated with 6-Minute Walk Distance, Distance-Saturation Product, and 6-Minute Walk Work in Patients with Lymphangioleiomyomatosis

Characteristics and Outcomes of Patients with LAM Receiving Sirolimus in France Based on Real-Life Data

Description des caractéristiques et de l’évolution clinique de la lymphangioléiomyomatose (LAM) chez les patientes traitées par sirolimus en France

Phenotypes in Pulmonary Hypertension

4D Flow Cardiac MRI to Assess Pulmonary Blood Flow in Patients with Pulmonary Arterial Hypertension Associated with Congenital Heart Disease

Thirty Years of Surgical Management of Pediatric Pulmonary Hypertension: Mid-Term Outcomes Following Reverse Potts Shunt and Transplantation

Percutaneous Atrial Septal Defect Closure in Patients with Pulmonary Arterial Hypertension

Bioreactance Assessment of Cardiac Output Lacks Reliability for the Follow-up of Patients with Pulmonary Hypertension

Deep Phenotyping of Unaffected Carriers of Pathogenic BMPR2 Variants Screened for Pulmonary Arterial Hypertension

Pulmonary Hypertension Induced by Right Pulmonary Artery Occlusion: Hemodynamic Consequences of Bmpr2 Mutation