Publications scientifiques
Voici les publications scientifiques relatives aux maladies respiratoires rares auxquelles les membres de la filière ont contribué, classées par groupes de pathologies (depuis juillet 2021).
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Pneumopathies interstitielles diffuses (PID)
Chronic Interstitial Lung Disease Associated with Systemic Lupus Erythematosus: A Multicentric Study of 89 Cases
Respirology 29, nᵒ 8 (mars 2024): 713‑21.
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Pneumopathies interstitielles diffuses (PID)
Total lung capacity is predictive of disease severity and survival in systemic sclerosis: A longitudinal analysis in 2347 patients from the French National Cohort Study
Journal of Autoimmunity 152 (mars 2025): 103391.
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Pneumopathies interstitielles diffuses (PID)
Efficacy and Safety of CFTR Modulators in Patients with Interstitial Lung Disease Caused by ABCA3 Transporter Deficiency
ERJ Open Research 11, nᵒ 2 (mars 2025)
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Pneumopathies interstitielles diffuses (PID)
Rare Genetic Interstitial Lung Diseases: A Pictorial Essay
European Respiratory Review 33, nᵒ 174 (novembre 2024)
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Pneumopathies interstitielles diffuses (PID)
A 24/7 Pilot Remote Emergency Multidisciplinary Discussion for Rapidly Progressive Interstitial Lung Disease: A 2-Year Experience
CHEST 167, nᵒ 1 (1 janvier 2025): 183‑87.
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Protéinose alvéolaire pulmonaire (PAP)
Recurrent Respiratory Papillomatosis in Adults with Lower Respiratory Tract Involvement: A Retrospective Study of the OrphaLung and GETIF Networks
European Respiratory Journal 65, nᵒ 3 (mars 2025)
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Protéinose alvéolaire pulmonaire (PAP)
Nocardia Infection in Patients With Anti–Granulocyte-Macrophage Colony-Stimulating Factor Autoantibodies: A Prospective Multicenter French Study
Open Forum Infectious Diseases 11, nᵒ 6 (juin 2024): ofae269.
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Maladies pulmonaires chroniques liées à l’environnement
Mortality in chronic pulmonary aspergillosis: a systematic review and individual patient data meta-analysis
The Lancet Infectious Diseases 25, nᵒ 3 (mars 2025): 312‑24.
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Maladies pulmonaires chroniques liées à l’environnement
Enhancing Antifungal Treatment for Chronic Cavitary Pulmonary Aspergillosis through the Addition of Endobronchial Valve Therapy
Respiratory Medicine Case Reports 52 (septembre 2024): 102106.
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Maladies pulmonaires chroniques liées à l’environnement
CT Imaging Assessment of Response to Treatment in Allergic Bronchopulmonary Aspergillosis in Adults With Bronchial Asthma
Chest 165, nᵒ 6 (février 2024): 1307‑18.