Publications scientifiques
Voici les publications scientifiques relatives aux maladies respiratoires rares auxquelles les membres de la filière ont contribué, classées par groupes de pathologies (depuis juillet 2021).
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Hypertension pulmonaire (HTP)
Chronic thromboembolic pulmonary hypertension and totally implantable central venous access systems
Eur Respir J. 2021 Jan 21;57(1):2002208. Doi: 10.1183/13993003.02208-2020.
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Hypertension pulmonaire (HTP)
Sleep-related breathing disorders and pulmonary hypertension
Eur Respir J. 2021 Jan 5;57(1):2002258. Doi: 10.1183/13993003.02258-2020.
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Hypertension pulmonaire (HTP)
Riociguat treatment in patients with pulmonary arterial hypertension : Final safety data from the EXPERT registry
Respir Med. 2020 Dec 3;177:106241. Doi: 10.1016/j.rmed.2020.106241.
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Maladies pulmonaires chroniques kystiques (LAM/MKPM)
COVID-19 in lymphangioleiomyomatosis: an international study of outcomes and impact of mTOR inhibition.
Chest. 2021 Dec 20:S0012-3692(21)05166-7.
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Maladies pulmonaires chroniques kystiques (LAM/MKPM)
Tuberous sclerosis complex for the pulmonologist
Eur Respir Rev. 2021 Aug 3;30(161):200348. Doi: 10.1183/16000617.0348-2020.
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Maladies pulmonaires chroniques kystiques (LAM/MKPM)
Combined pulmonary fibrosis and emphysema in alpha-1-antitrypsin deficiency
Respir Med Res. 2021 May;79:100819. Doi: 10.1016/j.resmer.2021.100819.
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Maladies pulmonaires chroniques kystiques (LAM/MKPM)
[Erratum to “Screening for alpha1-antitrypsin deficiency using dried blood spot: Assessment of the first 20 months” [Rev. Mal. Respir. 37 (2020) 633-43]]
Rev Mal Respir. 2021 Jan;38(1):125-126. Doi: 10.1016/j.rmr.2020.11.011.
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Maladies pulmonaires chroniques liées à l’environnement
Nebulised liposomal-amphotericin-B as maintenance therapy in ABPA: a randomised, multicentre, trial
Eur Respir J. 2021 Nov 11:2102218.
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Maladies pulmonaires chroniques liées à l’environnement
Medical algorithm: Aspergillus fumigatus components in the diagnosis of Allergic Bronchopulmonary Aspergillosis
Allergy. 2021 Jul 12. Doi: 10.1111/all.15001.
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Maladies pulmonaires chroniques liées à l’environnement
[Allergic Broncho-Pulmonary Aspergillosis (ABPA) in cystic fibrosis: Mechanisms, diagnosis and therapeutic options]
Rev Mal Respir. 2021 May;38(5):466-476. Doi: 10.1016/j.rmr.2021.04.004.