Publications scientifiques
Voici les publications scientifiques relatives aux maladies respiratoires rares auxquelles les membres de la filière ont contribué, classées par groupes de pathologies (depuis juillet 2021).
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Hypertension pulmonaire (HTP)
An endothelial activin A-bone morphogenetic protein receptor type 2 link is overdriven in pulmonary hypertension
Nat Commun. 2021 Mar 19;12(1):1720. Doi: 10.1038/s41467-021-21961-3.
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Hypertension pulmonaire (HTP)
Risk Stratification in Pulmonary Arterial Hypertension : Do Not Forget the Patient Perspective
Am J Respir Crit Care Med. 2021 Mar 15;203(6):675-677. Doi: 10.1164/rccm.202012-4350ED.
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Hypertension pulmonaire (HTP)
Riociguat treatment in patients with chronic thromboembolic pulmonary hypertension: Final safety data from the EXPERT registry
Respir Med. 2021 Mar;178:106220. Doi: 10.1016/j.rmed.2020.106220.
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Hypertension pulmonaire (HTP)
Characteristics and Long-term Outcomes of Pulmonary Venoocclusive Disease Induced by Mitomycin C.
Chest. 2021 Mar;159(3):1197-1207. Doi: 10.1016/j.chest.2020.09.238.
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Hypertension pulmonaire (HTP)
Reversible pulmonary hypertension associated with multivisceral Whipple’s disease
Eur Respir J. 2021 Feb 25;57(2):2003132. Doi: 10.1183/13993003.03132-2020.
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Hypertension pulmonaire (HTP)
Pulmonary Vascular Resistance in Pulmonary Arterial Hypertension: La Pièce de Résistance ?
Am J Respir Crit Care Med. 2021 Feb 15;203(4):524-525. Doi: 10.1164/rccm.202009-3664LE.
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Hypertension pulmonaire (HTP)
Targeting transforming growth factor-β receptors in pulmonary hypertension
Eur Respir J. 2021 Feb 4;57(2):2002341. Doi: 10.1183/13993003.02341-2020.
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Hypertension pulmonaire (HTP)
Pulmonary arterial hypertension in systemic sclerosis
Presse Med. 2021 Feb 3;50(1):104062. Doi: 10.1016/j.lpm.2021.104062.
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Hypertension pulmonaire (HTP)
Hemodynamic Response to Treatment and Outcomes in Pulmonary Hypertension Associated With Interstitial Lung Disease Versus Pulmonary Arterial Hypertension in Systemic Sclerosis : Data From a Study Identifying Prognostic Factors in Pulmonary Hypertension Associated With Interstitial Lung Disease
Arthritis Rheumatol. 2021 Feb;73(2):295-304. Doi: 10.1002/art.41512.
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Hypertension pulmonaire (HTP)
Kcnk3 Dysfunction Exaggerates The Development Of Pulmonary Hypertension Induced By Left Ventricular Pressure Overload
Cardiovasc Res. 2021 Jan 23: cvab016. Doi: 10.1093/cvr/cvab016.