Publications scientifiques
Voici les publications scientifiques relatives aux maladies respiratoires rares auxquelles les membres de la filière ont contribué, classées par groupes de pathologies (depuis juillet 2021).
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Hypertension pulmonaire (HTP)
Outcomes of patients with decreased arterial oxyhaemoglobin saturation on pulmonary arterial hypertension drugs
Eur Respir J. 2021 Nov 4;58(5):2004066.
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Hypertension pulmonaire (HTP)
Role of Store-Operated Ca2+ Entry in the Pulmonary Vascular Remodeling Occurring in Pulmonary Arterial Hypertension
Biomolecules. 2021 Nov 27;11(12):1781.
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Hypertension pulmonaire (HTP)
Sex and gender in pulmonary arterial hypertension
Eur Respir Rev. 2021 Nov 8;30(162):200330.
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Hypertension pulmonaire (HTP)
Pulmonary hypertension : A rare but severe complication of common variable immunodeficiency
Ann Allergy Asthma Immunol. 2021 Oct;127(4):512-513. Doi: 10.1016/j.anai.2021.06.016.
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Hypertension pulmonaire (HTP)
Association between Initial Treatment Strategy and Long-Term Survival in Pulmonary Arterial Hypertension
Am J Respir Crit Care Med. 2021 Oct 1;204(7):842-854. Doi: 10.1164/rccm.202009-3698OC.
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Hypertension pulmonaire (HTP)
Pulmonary Hypertension in Patients with Common Variable Immunodeficiency
J Clin Immunol. 2021 Oct;41(7):1549-1562. Doi: 10.1007/s10875-021-01064-w.
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Hypertension pulmonaire (HTP)
Investigating the association between ALK Receptor Tyrosine Kinase inhibitors and pulmonary arterial hypertension: a disproportionality analysis from the WHO pharmacovigilance database
Eur Respir J. 2021 Sep 29:2101576. Doi: 10.1183/13993003.01576-2021.
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Hypertension pulmonaire (HTP)
Mendelian randomisation and experimental medicine approaches to IL-6 as a drug target in PAH
Eur Respir J. 2021 Sep 29:2002463. Doi: 10.1183/13993003.02463-2020.
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Hypertension pulmonaire (HTP)
Severe pulmonary hypertension associated with chronic obstructive pulmonary disease: A prospective French multicenter cohort
J Heart Lung Transplant. 2021 Sep;40(9):1009-1018. Doi: 10.1016/j.healun.2021.04.021.
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Hypertension pulmonaire (HTP)
A CELSR1 variant in a patient with pulmonary arterial hypertension
Clin Genet. 2021 Aug 25. Doi: 10.1111/cge.14046.