Publications scientifiques
Voici les publications scientifiques relatives aux maladies respiratoires rares auxquelles les membres de la filière ont contribué, classées par groupes de pathologies (depuis juillet 2021).
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Anomalies du développement pulmonaire (ADP)
Thoracoscopic surgery for congenital lung malformations: Does previous infection really matter?
J Pediatr Surg. 2021 Nov;56(11):1982-1987.
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Anomalies du développement pulmonaire (ADP)
Predicting the risk of respiratory distress in newborns with congenital pulmonary malformations
Eur Respir J. 2021 Jul 15:2100949.
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Anomalies du développement pulmonaire (ADP)
Thoracoscopic surgery for congenital lung malformations : Does previous infection really matter?
J Pediatr Surg. 2021 Jan 27: S0022-3468(21)00086-5.
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Anomalies du développement pulmonaire (ADP)
Intravenous pulses of methylprednisolone for infants with severe bronchopulmonary dysplasia and respiratory support after 3 months of age
Pediatr Pulmonol. 2021 Jan;56(1):74-82.
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Anomalies du contrôle respiratoire
Obstructive Apneas in a Mouse Model of Congenital Central Hypoventilation Syndrome
Am J Respir Crit Care Med. 2021 Nov 15;204(10):1200-1210.
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Dilatation des bronches ou bronchectasies (non CF, non DCP)
Management of early infection with Pseudomonas aeruginosa in adults with bronchiectasis: A survey of French pulmonologist’s practices
Respir Med Res. 2021 Sep 9;80:100859.
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Dilatation des bronches ou bronchectasies (non CF, non DCP)
Robotic lobectomy in children with severe bronchiectasis: A worthwhile new technology
J Pediatr Surg. 2021 Sep;56(9):1606-1610.
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Dilatation des bronches ou bronchectasies (non CF, non DCP)
European Respiratory Society guidelines for the management of children and adolescents with bronchiectasis
Eur Respir J. 2021 Aug 26;58(2):2002990.
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Dyskinésies ciliaires primitives (DCP)
Impact of a rare respiratory diseases reference centre set-up on primary ciliary dyskinesia care pathway
Eur Respir J. 2022 Jan 13;59(1):2102413
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Dyskinésies ciliaires primitives (DCP)
Ciliary Videomicroscopy: A Long Beat from the European Respiratory Society Guidelines to the Recognition as a Confirmatory Test for Primary Ciliary Dyskinesia
Diagnostics (Basel). 2021 Sep 17;11(9):1700