Publications scientifiques
Voici les publications scientifiques relatives aux maladies respiratoires rares auxquelles les membres de la filière ont contribué, classées par groupes de pathologies (depuis juillet 2021).
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Pneumopathies interstitielles diffuses (PID)
Targeting IL-5/5R for the treatment of idiopathic chronic eosinophilic pneumonia.
J Allergy Clin Immunol Pract. 2022 Dec 26:S2213-2198(22)01335-6.
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Pneumopathies interstitielles diffuses (PID)
Criteria for Progressive Pulmonary Fibrosis: Getting the Horse Ready for the Cart.
Am J Respir Crit Care Med. 2023 Jan 1;207(1):11-13.
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Pneumopathies interstitielles diffuses (PID)
Clinical features and outcomes of patients with myositis associated-interstitial lung disease.
Front Med (Lausanne). 2023 Jan 9;9:1096203.
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Pneumopathies interstitielles diffuses (PID)
Deciphering an isolated lung phenotype of NKX2-1 frameshift pathogenic variant.
Front Pediatr. 2023 Jan 17;10:978598.
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Pneumopathies interstitielles diffuses (PID)
COVID-19 in patients with pulmonary alveolar proteinosis: a European multicentre study.
ERJ Open Res. 2023 Jan 3;9(1):00199-2022.
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Pneumopathies interstitielles diffuses (PID)
Long-term evolution of neuroendocrine cell hyperplasia of infancy: the FRENCHI findings.
Eur J Pediatr. 2023 Feb;182(2):949-956.
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Fibrose pulmonaire - FPI
Study protocol of an international patient-led registry in patients with pulmonary fibrosis using online home monitoring: I-FILE.
BMC Pulm Med. 2023 Feb 2;23(1):51.
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Pneumopathies interstitielles diffuses (PID)
Inherited pulmonary surfactant metabolism disorders in Argentina: Differences between patients with SFTPC and ABCA3 variants.
Pediatr Pulmonol. 2023 Feb;58(2):540-549.
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Maladies pulmonaires chroniques liées à l’environnement
Nebulised liposomal amphotericin-B as maintenance therapy in allergic bronchopulmonary aspergillosis: a randomised, multicentre trial.
Eur Respir J. 2022 Jun 16;59(6):2102218.
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Maladies pulmonaires chroniques liées à l’environnement
Reply to: Nebulised liposomal amphotericin-B: a promising strategy for preventing ABPA relapse.
Eur Respir J. 2022 Nov 24;60(5):2201678.