Publications scientifiques
Voici les publications scientifiques relatives aux maladies respiratoires rares auxquelles les membres de la filière ont contribué, classées par groupes de pathologies (depuis juillet 2021).
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Pneumopathies interstitielles diffuses (PID)
Meta-Analysis of Effect of Nintedanib on Reducing FVC Decline Across Interstitial Lung Diseases.
Adv Ther. 2022 Jul;39(7):3392-3402.
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Pneumopathies interstitielles diffuses (PID)
FGF19 Is Downregulated in Idiopathic Pulmonary Fibrosis and Inhibits Lung Fibrosis in Mice.
Am J Respir Cell Mol Biol. 2022 Aug;67(2):173-187.
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Pneumopathies interstitielles diffuses (PID)
Small Airways in Pulmonary Fibrosis: Revisiting an Old Question with New Tools.
Am J Respir Crit Care Med. 2022 Aug 15;206(4):516-517.
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Pneumopathies interstitielles diffuses (PID)
Syndrome of Combined Pulmonary Fibrosis and Emphysema: An Official ATS/ERS/JRS/ALAT Research Statement.
Am J Respir Crit Care Med. 2022 Aug 15;206(4):e7-e41.
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Pneumopathies interstitielles diffuses (PID)
French national cohort of neuroendocrine cell hyperplasia of infancy (FRENCHI) study: diagnosis and initial management.
Eur J Pediatr. 2022 Aug;181(8):3067-3073.
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Pneumopathies interstitielles diffuses (PID)
Variable Expression of Lung Disease Due to a Novel Homozygous ABCA3 Variant.
Pediatr Allergy Immunol Pulmonol. 2022 Sep;35(3):124-128.
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Pneumopathies interstitielles diffuses (PID)
Pleuroparenchymal fibroelastosis.
Curr Opin Pulm Med. 2022 Sep 1;28(5):432-440.
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Pneumopathies interstitielles diffuses (PID)
Chest ultrasound findings in usual interstitial pneumonia patterns: a pilot study.
Monaldi Arch Chest Dis. 2022 Sep 7.
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Pneumopathies interstitielles diffuses (PID)
Genetic testing in interstitial lung disease: An international survey.
Respirology. 2022 Sep;27(9):747-757.
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Pneumopathies interstitielles diffuses (PID)
New insights into methylome alterations and consequences during myofibroblastic differentiation in pulmonary fibrosis.
Eur Respir J. 2022 Sep 29;60(3):2201536.