Publications scientifiques
Voici les publications scientifiques relatives aux maladies respiratoires rares auxquelles les membres de la filière ont contribué, classées par groupes de pathologies (depuis juillet 2021).
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Fibrose pulmonaire - FPI 02/08/23
Cyclophosphamide added to glucocorticoids in acute exacerbation of idiopathic pulmonary fibrosis (EXAFIP): a randomised, double-blind, placebo-controlled, phase 3 trial
Lancet Respir Med. 2021 Sep 7: S2213-2600(21)00354-4.
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Fibrose pulmonaire - FPI 02/08/23
IC4 : a new combined predictive index of mortality in idiopathic pulmonary fibrosis
Panminerva Med. 2021 Jan 26.
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Hypertension pulmonaire (HTP) 02/08/23
Phenotypic Diversity of Vascular Smooth Muscle Cells in Pulmonary Arterial Hypertension: Implications for Therapy
Chest. 2022 Jan;161(1):219-231.
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Fibrose pulmonaire - FPI 02/08/23
NADPH oxidase DUOX1 sustains TGF-β1 signalling and promotes lung fibrosis
Eur Respir J. 2021 Jan 14;57(1):1901949.
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Hypertension pulmonaire (HTP) 02/08/23
Double-lung transplantation followed by delayed percutaneous repair for atrial septal defect-associated pulmonary arterial hypertension
Eur Respir J. 2022 Jan 20;59(1):2102388.
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Hypertension pulmonaire (HTP) 02/08/23
Biological heterogeneity in idiopathic pulmonary arterial hypertension identified through unsupervised transcriptomic profiling of whole blood
Nat Commun. 2021 Dec 7;12(1):7104.
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Hypertension pulmonaire (HTP) 02/08/23
Hospital costs of Balloon Pulmonary Angioplasty (BPA) procedure and management for CTEPH patients: An observational study based on the French national hospital discharge database (PMSI)
PLoS One. 2021 Dec 7;16(12):e0260483.
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Hypertension pulmonaire (HTP) 02/08/23
Outcomes of patients with decreased arterial oxyhaemoglobin saturation on pulmonary arterial hypertension drugs
Eur Respir J. 2021 Nov 4;58(5):2004066.
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Hypertension pulmonaire (HTP) 02/08/23
Role of Store-Operated Ca2+ Entry in the Pulmonary Vascular Remodeling Occurring in Pulmonary Arterial Hypertension
Biomolecules. 2021 Nov 27;11(12):1781.
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Hypertension pulmonaire (HTP) 02/08/23
Sex and gender in pulmonary arterial hypertension
Eur Respir Rev. 2021 Nov 8;30(162):200330.