Publications scientifiques
Voici les publications scientifiques relatives aux maladies respiratoires rares auxquelles les membres de la filière ont contribué, classées par groupes de pathologies (depuis juillet 2021).
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Sarcoïdose
Sarcoidosis-Associated Pulmonary Hypertension
Journal of Clinical Medicine 13, nᵒ 7 (avril 2024): 2054
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Sarcoïdose
Sarcoidosis and Emergency Hospitalization
CHEST 167, nᵒ 1 (janvier 2025): 164‑71.
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Sarcoïdose
Cystic Lung in Sarcoidosis: Clinico-Radiologic Characteristic and Evolution
Respirology 29, nᵒ 12 (décembre 2024): 1067‑76.
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Sarcoïdose
High-Resolution CT Phenotypes in Pulmonary Sarcoidosis: A Multinational Delphi Consensus Study
The Lancet. Respiratory Medicine 12, nᵒ 5 (mai 2024): 409‑18.
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Sarcoïdose
Favorable prognosis of subcutaneous sarcoidosis: French cohort of 80 patients compared with dermal sarcoidosis
Journal of the American Academy of Dermatology 92, nᵒ 2 (février 2025): 329‑32.
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Pneumopathies interstitielles diffuses (PID)
Childhood Interstitial Lung Disease Survivors in Adulthood: A European Collaborative Study
The European Respiratory Journal 65, nᵒ 2 (février 2025): 2400680
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Pneumopathies interstitielles diffuses (PID)
Bi-Allelic LAMP3 Variants in Childhood Interstitial Lung Disease: A Surfactant-Related Disease
EBioMedicine 113 (février 2025): 105626.
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Fibrose pulmonaire - FPI
A Roadmap to Precision Treatments for Familial Pulmonary Fibrosis
EBioMedicine 104 (juin 2024): 105135
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Pneumopathies interstitielles diffuses (PID)
Pulmonary Fibrosis May Begin in Infancy: From Childhood to Adult Interstitial Lung Disease
Thorax 79, nᵒ 12 (novembre 2024): 1162‑72
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Pneumopathies interstitielles diffuses (PID)
Surfactant Protein B Deficiency: The RespiRare Cohort
Thorax 80, nᵒ 2 (janvier 2025): 109‑12.