Publications - Page 18 sur 43 - RespiFIL - Filière de santé des maladies respiratoires rares

Voici les publications scientifiques relatives aux maladies respiratoires rares auxquelles les membres de la filière ont contribué, classées par groupes de pathologies (depuis juillet 2021).

Hypertension pulmonaire (HTP) 31/08/23
Molecular Function and Contribution of TBX4 in Development and Disease.

Karolak JA, Welch CL, Mosimann C, Bzdęga K, West JD, Montani D, Eyries M, Mullen MP, Abman SH, Prapa M, Gräf S, Morrell NW, Hemnes AR, Perros F, Hamid R, Logan MPO, Whitsett J, Galambos C, Stankiewicz P, Chung WK, Austin ED.

Am J Respir Crit Care Med. 2023 Apr 1;207(7):855-864.
Hypertension pulmonaire (HTP) 31/08/23
Sotatercept for the treatment of pulmonary arterial hypertension: PULSAR open-label extension

Humbert M, McLaughlin V, Gibbs JSR, Gomberg-Maitland M, Hoeper MM, Preston IR, Souza R, Waxman AB, Ghofrani HA, Escribano Subias P, Feldman J, Meyer G, Montani D, Olsson KM, Manimaran S, de Oliveira Pena J, Badesch DB.

Eur Respir J. 2023 Jan 6;61(1):2201347.
Hypertension pulmonaire (HTP) 31/08/23
Phase 3 Trial of Sotatercept for Treatment of Pulmonary Arterial Hypertension

Hoeper MM, Badesch DB, Ghofrani HA, Gibbs JSR, Gomberg-Maitland M, McLaughlin VV, Preston IR, Souza R, Waxman AB, Grünig E, Kopeć G, Meyer G, Olsson KM, Rosenkranz S, Xu Y, Miller B, Fowler M, Butler J, Koglin J, de Oliveira Pena J, Humbert M; STELLAR Trial Investigators.

N Engl J Med. 2023 Apr 20;388(16):1478-1490.
Pneumopathies interstitielles diffuses (PID) 31/08/23
Inverted direct allorecognition triggers early donor-specific antibody responses after transplantation.

Charmetant X, Chen CC, Hamada S, Goncalves D, Saison C, Rabeyrin M, Rabant M, Duong van Huyen JP, Koenig A, Mathias V, Barba T, Lacaille F, le Pavec J, Brugière O, Taupin JL, Chalabreysse L, Mornex JF, Couzi L, Graff-Dubois S, Jeger-Madiot R, Tran-Dinh A, Mordant P, Paidassi H, Defrance T, Morelon E, Badet L, Nicoletti A, Dubois V, Thaunat O.

Sci Transl Med. 2022 Sep 21;14(663):eabg1046.
Pneumopathies interstitielles diffuses (PID) 31/08/23
Lung transplantation for interstitial lung disease in idiopathic inflammatory myositis: A cohort study.

Rivière A, Picard C, Berastegui C, Mora VM, Bunel V, Godinas L, Salvaterra E, Rossetti V, Savale L, Israel-Biet D, Demant X, Bermudez J, Meloni F, Jaksch P, Magnusson J, Beaumont L, Perch M, Mornex JF, Knoop C, Aubert JD, Hervier B, Nunes H, Humbert M, Gottlieb J, Uzunhan Y, Le Pavec J.

Am J Transplant. 2022 Dec;22(12):2990-3001.
Dilatation des bronches ou bronchectasies (non CF, non DCP) 31/08/23
[Updated indications and contraindications in 2022 for lung transplantation in France].

Le Pavec J, Pison C, Hirschi S, Bunel V, Mordant P, Brugière O, Le Guen M, Olland A, Coiffard B, Renaud-Picard B, Tissot A, Brioude G, Borie R, Crestani B, Deslée G, Stelianides S, Mal H, Schuller A, Falque L, Lorillon G, Tazi A, Burgel PR, Grenet D, De Miranda S, Bergeron A, Launay D, Cottin V, Nunes H, Valeyre D, Uzunhan Y, Prévot G, Sitbon O, Montani D, Savale L, Humbert M, Fadel E, Mercier O, Mornex JF, Dauriat G, Reynaud-Gaubert M.

Rev Mal Respir. 2022 Dec;39(10):855-872.
Pneumopathies interstitielles diffuses (PID) 31/08/23
Study design and rationale for the TETON phase 3, randomised, controlled clinical trials of inhaled treprostinil in the treatment of idiopathic pulmonary fibrosis.

Nathan SD, Behr J, Cottin V, Lancaster L, Smith P, Deng CQ, Pearce N, Bell H, Peterson L, Flaherty KR.

BMJ Open Respir Res. 2022 Jul;9(1):e001310.
Pneumopathies interstitielles diffuses (PID) 31/08/23
Meta-Analysis of Effect of Nintedanib on Reducing FVC Decline Across Interstitial Lung Diseases.

Bonella F, Cottin V, Valenzuela C, Wijsenbeek M, Voss F, Rohr KB, Stowasser S, Maher TM. Adv Ther. 2022 Jul;39(7):3392-3402.

Adv Ther. 2022 Jul;39(7):3392-3402.
Pneumopathies interstitielles diffuses (PID) 31/08/23
FGF19 Is Downregulated in Idiopathic Pulmonary Fibrosis and Inhibits Lung Fibrosis in Mice.

Justet A, Ghanem M, Boghanim T, Hachem M, Vasarmidi E, Jaillet M, Vadel A, Joannes A, Mordant P, Bonniaud P, Kolb M, Ling L, Cazes A, Mal H, Mailleux A, Crestani B.

Am J Respir Cell Mol Biol. 2022 Aug;67(2):173-187.
Pneumopathies interstitielles diffuses (PID) 31/08/23
Small Airways in Pulmonary Fibrosis: Revisiting an Old Question with New Tools.

Cottin V.

Am J Respir Crit Care Med. 2022 Aug 15;206(4):516-517.

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Molecular Function and Contribution of TBX4 in Development and Disease.

Sotatercept for the treatment of pulmonary arterial hypertension: PULSAR open-label extension

Phase 3 Trial of Sotatercept for Treatment of Pulmonary Arterial Hypertension

Inverted direct allorecognition triggers early donor-specific antibody responses after transplantation.

Lung transplantation for interstitial lung disease in idiopathic inflammatory myositis: A cohort study.

[Updated indications and contraindications in 2022 for lung transplantation in France].

Study design and rationale for the TETON phase 3, randomised, controlled clinical trials of inhaled treprostinil in the treatment of idiopathic pulmonary fibrosis.

Meta-Analysis of Effect of Nintedanib on Reducing FVC Decline Across Interstitial Lung Diseases.

FGF19 Is Downregulated in Idiopathic Pulmonary Fibrosis and Inhibits Lung Fibrosis in Mice.

Small Airways in Pulmonary Fibrosis: Revisiting an Old Question with New Tools.