Publications scientifiques
Voici les publications scientifiques relatives aux maladies respiratoires rares auxquelles les membres de la filière ont contribué, classées par groupes de pathologies (depuis juillet 2021).
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Hypertension pulmonaire (HTP)
Risk Stratification and Treatment Goals in Pulmonary Arterial Hypertension
European Respiratory Journal, octobre 2024.
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Hypertension pulmonaire (HTP)
Treatment Algorithm for Pulmonary Arterial Hypertension
European Respiratory Journal, octobre 2024, 2401325.
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Hypertension pulmonaire (HTP)
Sacubitril/Valsartan Has an Underestimated Impact on the Right Ventricle in Patients with Sleep-Disordered Breathing, Especially Central Sleep Apnoea Syndrome
Archives of Cardiovascular Diseases 117, nᵒ 6‑7 (juin 2024): 409‑16.
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Hypertension pulmonaire (HTP)
Pulmonary Hypertension in Connective Tissue Diseases Other than Systemic Sclerosis
Seminars in Respiratory and Critical Care Medicine 45, nᵒ 3 (juin 2024): 419‑34.
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Hypertension pulmonaire (HTP)
Medication Adherence, Related Factors and Outcomes among Patients with Pulmonary Arterial Hypertension or Chronic Thromboembolic Pulmonary Hypertension: A Systematic Review
European Respiratory Review 33, nᵒ 173 (juillet 2024).
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Hypertension pulmonaire (HTP)
Initial Therapy in Patients with Pulmonary Arterial Hypertension and Cardiovascular Comorbidities
The European Respiratory Journal, janvier 2025, 2400895.
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Hypertension pulmonaire (HTP)
Risk Stratification Refinements with Inclusion of Haemodynamic Variables at Follow-up in Patients with Pulmonary Arterial Hypertension
The European Respiratory Journal 64, nᵒ 3 (septembre 2024): 2400197
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Hypertension pulmonaire (HTP)
Evidence and unresolved questions in pulmonary hypertension: Insights from the 5th French Pulmonary Hypertension Network Meeting
Respiratory Medicine and Research 86 (novembre 2024): 101123.
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Hypertension pulmonaire (HTP)
Dispositif médical pour le drainage thoracique : optimisation de la prise en charge thérapeutique par l’élaboration multidisciplinaire d’un arbre décisionnel
Le Pharmacien Clinicien 59, nᵒ 2 (juin 2024): e179
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Hyperplasie des cellules neuroendocrines du nourrisson (NEHI)
Diagnostic Evaluation and Clinical Findings in Children with Persistent Tachypnea of Infancy/Neuroendocrine Cell Hyperplasia of Infancy : A European Multicenter Retrospective Study
Chest, mars 2025, S0012-3692(25)00272-7.