Publications scientifiques
Voici les publications scientifiques relatives aux maladies respiratoires rares auxquelles les membres de la filière ont contribué, classées par groupes de pathologies (depuis juillet 2021).
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Hypertension pulmonaire (HTP)
Characteristics and Outcomes of Gemcitabine-Associated Pulmonary Hypertension
ERJ Open Research 10, nᵒ 3 (mai 2024): 00654‑02023.
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Hypertension pulmonaire (HTP)
Consistent Safety and Efficacy of Sotatercept for Pulmonary Arterial Hypertension in BMPR2 Mutation Carriers and Noncarriers: A Planned Analysis of Phase 2, Double-Blind, Placebo-Controlled Clinical Trial (PULSAR)
American Journal of Respiratory and Critical Care Medicine, mars 2025
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Hypertension pulmonaire (HTP)
Unmet Need in Pulmonary Hypertension-Associated Interstitial Lung Disease (PH-ILD): A Clinician Survey of Real-World Management of PH-ILD in Europe
ERJ Open Research 10, nᵒ 4 (juillet 2024): 00039‑02024.
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Hypertension pulmonaire (HTP)
Prognostic Relevance of Exercise Pulmonary Hypertension: Results of the Multicentre PEX-NET Clinical Research Collaboration
The European Respiratory Journal 64, nᵒ 6 (décembre 2024): 2400698.
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Hypertension pulmonaire (HTP)
Primum Non Nocere, Secundum Cavere, Tertium Sanare: Lessons on the Management of Pulmonary Hypertension Associated with COPD
European Respiratory Journal 63, nᵒ 6 (juin 2024).
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Hypertension pulmonaire (HTP)
Development and Validation of a Code-Based Algorithm Using in-Hospital Medical Records to Identify Patients with Pulmonary Arterial Hypertension in a French Healthcare Database
ERJ Open Research 10, nᵒ 4 (août 2024): 00109‑02024.
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Hypertension pulmonaire (HTP)
Embracing the Challenges of Neonatal and Paediatric Pulmonary Hypertension
European Respiratory Journal, octobre 2024.
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Hypertension pulmonaire (HTP)
MK-5475, an Inhaled Soluble Guanylate Cyclase Stimulator, for Treatment of Pulmonary Arterial Hypertension: The INSIGNIA-PAH Study
The European Respiratory Journal 64, nᵒ 5 (novembre 2024): 2401110.
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Hypertension pulmonaire (HTP)
Integrative Multiomics in the Lung Reveals a Protective Role of Asporin in Pulmonary Arterial Hypertension
Circulation 150, nᵒ 16 (août 2024): 1268‑87.
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Hypertension pulmonaire (HTP)
Riociguat in Pulmonary Arterial Hypertension: Application of the 4-Strata COMPERA 2.0 Risk Assessment Tool in the PATENT Studies
Respiratory Medicine 236 (janvier 2025): 107910