Publications scientifiques
Voici les publications scientifiques relatives aux maladies respiratoires rares auxquelles les membres de la filière ont contribué, classées par groupes de pathologies (depuis juillet 2021).
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Pneumopathies interstitielles diffuses (PID)
Cardiopulmonary exercise testing in interstitial lung diseases and the value of ventilatory efficiency
Eur Respir Rev. 2021 Nov 30;30(162):200355.
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Pneumopathies interstitielles diffuses (PID)
RaDiCo, the French national research program on rare disease cohorts
Orphanet J Rare Dis. 2021 Oct 29;16(1):454.
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Pneumopathies interstitielles diffuses (PID)
MUC5B promoter variant rs35705950 and rheumatoid arthritis associated interstitial lung disease survival and progression
Semin Arthritis Rheum. 2021 Oct;51(5):996-1004. Doi: 10.1016/j.semarthrit.2021.07.002.
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Pneumopathies interstitielles diffuses (PID)
Variability in Global Prevalence of Interstitial Lung Disease
Front Med (Lausanne). 2021 Nov 4;8:751181.
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Pneumopathies interstitielles diffuses (PID)
Nintedanib in idiopathic and secondary pleuroparenchymal fibroelastosis
Orphanet J Rare Dis. 2021 Oct 9;16(1):419.
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Pneumopathies interstitielles diffuses (PID)
Diagnosis yield and safety of surgical biopsy in interstitial lung diseases: a prospective study
Ann Thorac Surg. 2021 Sep 29: S0003-4975(21)01672-6. Doi: 10.1016/j.athoracsur.2021.08.056.
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Pneumopathies interstitielles diffuses (PID)
Methionine supplementation for multi-organ dysfunction in MetRS-related pulmonary alveolar proteinosis
Eur Respir J. 2021 Sep 9:2101554. Doi: 10.1183/13993003.01554-2021.
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Pneumopathies interstitielles diffuses (PID)
[18F]FMISO PET/CT imaging of hypoxia as a non-invasive biomarker of disease progression and therapy efficacy in a preclinical model of pulmonary fibrosis: comparison with the [18F]FDG PET/CT approach
Eur J Nucl Med Mol Imaging. 2021 Sep;48(10):3058-3074. Doi: 10.1007/s00259-021-05209-2.
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Pneumopathies interstitielles diffuses (PID)
A call for evidence in connective tissue diseases-associated interstitial lung disease
Joint Bone Spine. 2021 Sep 15;89(1):105274. Doi: 10.1016/j.jbspin.2021.105274.
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Pneumopathies interstitielles diffuses (PID)
Early diagnosis of fibrotic interstitial lung disease: challenges and opportunities
Lancet Respir Med. 2021 Sep;9(9):1065-1076. Doi: 10.1016/S2213-2600(21)00017-5.