Publications scientifiques
Voici les publications scientifiques relatives aux maladies respiratoires rares auxquelles les membres de la filière ont contribué, classées par groupes de pathologies (depuis juillet 2021).
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Hypertension pulmonaire (HTP)
Combination Therapy with STAT3 Inhibitor Enhances SERCA2a-Induced BMPR2 Expression and Inhibits Pulmonary Arterial Hypertension
Int J Mol Sci. 2021 Aug 24;22(17):9105. Doi: 10.3390/ijms22179105.
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Hypertension pulmonaire (HTP)
Serum and pulmonary uric acid in pulmonary arterial hypertension
Eur Respir J. 2021 Aug 5;58(2):2000332. Doi: 10.1183/13993003.00332-2020.
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Hypertension pulmonaire (HTP)
Association between Leflunomide and Pulmonary Hypertension
Ann Am Thorac Soc. 2021 Aug;18(8):1306-1315. Doi: 10.1513/AnnalsATS.202008-913OC.
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Hypertension pulmonaire (HTP)
Screening for pulmonary arterial hypertension in adults carrying a BMPR2 mutation
Eur Respir J. 2021 Jul 22;58(1):2004229. Doi: 10.1183/13993003.04229-2020.
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Hypertension pulmonaire (HTP)
Phenotypic Diversity of Vascular Smooth Muscle Cells in Pulmonary Arterial Hypertension: Implications for Therapy
Chest. 2021 Aug 12: S0012-3692(21)03667-9. Doi: 10.1016/j.chest.2021.08.040.
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Hypertension pulmonaire (HTP)
Regulation of the Methylation and Expression Levels of the BMPR2 Gene by SIN3a as a Novel Therapeutic Mechanism in Pulmonary Arterial Hypertension
Circulation. 2021 Jul 6;144(1):52-73. Doi: 10.1161/CIRCULATIONAHA.120.047978.
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Hypertension pulmonaire (HTP)
Pulmonary hypertension associated with neurofibromatosis type 2
Pulm Circ. 2021 Jul 5;11(3):20458940211029550. Doi: 10.1177/20458940211029550.
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Hypertension pulmonaire (HTP)
Lung and heart-lung transplantation for children with PAH: Dramatic benefits from the implementation of a high-priority allocation program in France
J Heart Lung Transplant. 2021 Jul;40(7):652-661. Doi: 10.1016/j.healun.2021.03.013.
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Hypertension pulmonaire (HTP)
Right Ventricle Remodeling Metabolic Signature in Experimental Pulmonary Hypertension Models of Chronic Hypoxia and Monocrotaline Exposure
Cells. 2021 Jun 21;10(6):1559. Doi: 10.3390/cells10061559.
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Hypertension pulmonaire (HTP)
ERS statement on chronic thromboembolic pulmonary hypertension
Eur Respir J. 2021 Jun 17;57(6):2002828. Doi: 10.1183/13993003.02828-2020.