Publications - Page 40 sur 57 - RespiFIL - Filière de santé des maladies respiratoires rares

Voici les publications scientifiques relatives aux maladies respiratoires rares auxquelles les membres de la filière ont contribué, classées par groupes de pathologies (depuis juillet 2021).

Hypertension pulmonaire (HTP)
Quantifying leg muscle deoxygenation during incremental cycling in hypoxemic patients with fibrotic interstitial lung disease.

Marillier M, Bernard AC, Verges S, Moran-Mendoza O, Neder JA.

Clin Physiol Funct Imaging. 2022 Dec 29.
Hypertension pulmonaire (HTP)
Biomarkers of haemodynamic severity of systemic sclerosis-associated pulmonary arterial hypertension by serum proteome analysis.

Sanges S, Rice L, Tu L, Valenzi E, Cracowski JL, Montani D, Mantero JC, Ternynck C, Marot G, Bujor AM, Hachulla E, Launay D, Humbert M, Guignabert C, Lafyatis R.

Ann Rheum Dis. 2022 Dec 5:ard-2022-223237.
Hypertension pulmonaire (HTP)
Identifying new drugs associated with pulmonary arterial hypertension: A WHO pharmacovigilance database disproportionality analysis.

Hlavaty A, Roustit M, Montani D, Chaumais MC, Guignabert C, Humbert M, Cracowski JL, Khouri C.

Br J Clin Pharmacol. 2022 Dec;88(12):5227-5237.
Hypertension pulmonaire (HTP)
Lipidomic Profile Analysis of Lung Tissues Revealed Lipointoxication in Pulmonary Veno-Occlusive Disease.

Khoury S, Beauvais A, Colas J, Saint-Martin Willer A, Perros F, Humbert M, Vandebrouck C, Montani D, Ferreira T, Antigny F.

Biomolecules. 2022 Dec 14;12(12):1878.
Hypertension pulmonaire (HTP)
First Genotype-Phenotype Study in TBX4 Syndrome: Gain-of-Function Mutations Causative for Lung Disease.

Prapa M, Lago-Docampo M, Swietlik EM, Montani D, Eyries M, Humbert M, Welch CL, Chung WK, Berger RMF, Bogaard HJ, Danhaive O, Escribano-Subías P, Gall H, Girerd B, Hernandez-Gonzalez I, Holden S, Hunt D, Jansen SMA, Kerstjens-Frederikse W, Kiely DG, Lapunzina P, McDermott J, Moledina S, Pepke-Zaba J, Polwarth GJ, Schotte G, Tenorio-Castaño J, Thompson AAR, Wharton J, Wort SJ, Megy K, Mapeta R, Treacy CM, Martin JM, Li W, Swift AJ, Upton PD, Morrell NW, Gräf S, Valverde D; NIHR BioResource for Translational Research–Rare Diseases; National Cohort Study of Idiopathic and Heritable PAH; PAH Biobank Enrolling Centers’ Investigators.

Am J Respir Crit Care Med. 2022 Dec 15;206(12):1522-1533.
Hypertension pulmonaire (HTP)
Interest of TAPSE/sPAP ratio for noninvasive pulmonary arterial hypertension risk assessment.

Fauvel C, Raitiere O, Boucly A, De Groote P, Renard S, Bertona J, Lamblin N, Artaud-Macari E, Viacroze C, Schleifer D, Dominique S, Pichon J, Jais X, Montani D, Sitbon O, Savale L, Humbert M, Bauer F.

J Heart Lung Transplant. 2022 Dec;41(12):1761-1772.
Hypertension pulmonaire (HTP)
Cytokines as Prognostic Biomarkers in Pulmonary Arterial Hypertension.

Boucly A, Tu L, Guignabert C, Rhodes C, De Groote P, Prévot G, Bergot E, Bourdin A, Beurnier A, Roche A, Jevnikar M, Jaïs X, Montani D, Wilkins MR, Humbert M, Sitbon O, Savale L.

Eur Respir J. 2022 Dec 22:2201232.
Hypertension pulmonaire (HTP)
Involvement of SUR2/Kir6.1 channel in the physiopathology of pulmonary arterial hypertension.

Le Ribeuz H, Masson B, Dutheil M, Boët A, Beauvais A, Sabourin J, De Montpreville VT, Capuano V, Mercier O, Humbert M, Montani D, Antigny F.

Front Cardiovasc Med. 2023 Jan 10;9:1066047.
Hypertension pulmonaire (HTP)
Sotatercept for the treatment of pulmonary arterial hypertension: PULSAR open-label extension.

Humbert M, McLaughlin V, Gibbs JSR, Gomberg-Maitland M, Hoeper MM, Preston IR, Souza R, Waxman AB, Ghofrani HA, Escribano Subias P, Feldman J, Meyer G, Montani D, Olsson KM, Manimaran S, de Oliveira Pena J, Badesch DB.

Eur Respir J. 2023 Jan 6;61(1):2201347.
Hypertension pulmonaire (HTP)
In-depth characterization of pulmonary arterial hypertension in mixed connective tissue disease: a French national multicenter study.

Chaigne B, Chevalier K, Boucly A, Agard C, Baudet A, Bourdin A, Chabanne C, Cottin V, Fesler P, Goupil F, Jego P, Launay D, Lévesque H, Maurac A, Mohamed S, Tromeur C, Rottat L, Sitbon O, Humbert M, Mouthon L.

Rheumatology (Oxford). 2023 Feb 2:kead055.

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Quantifying leg muscle deoxygenation during incremental cycling in hypoxemic patients with fibrotic interstitial lung disease.

Biomarkers of haemodynamic severity of systemic sclerosis-associated pulmonary arterial hypertension by serum proteome analysis.

Identifying new drugs associated with pulmonary arterial hypertension: A WHO pharmacovigilance database disproportionality analysis.

Lipidomic Profile Analysis of Lung Tissues Revealed Lipointoxication in Pulmonary Veno-Occlusive Disease.

First Genotype-Phenotype Study in TBX4 Syndrome: Gain-of-Function Mutations Causative for Lung Disease.

Interest of TAPSE/sPAP ratio for noninvasive pulmonary arterial hypertension risk assessment.

Cytokines as Prognostic Biomarkers in Pulmonary Arterial Hypertension.

Involvement of SUR2/Kir6.1 channel in the physiopathology of pulmonary arterial hypertension.

Sotatercept for the treatment of pulmonary arterial hypertension: PULSAR open-label extension.

In-depth characterization of pulmonary arterial hypertension in mixed connective tissue disease: a French national multicenter study.