Publications - Page 35 sur 43 - RespiFIL - Filière de santé des maladies respiratoires rares

Voici les publications scientifiques relatives aux maladies respiratoires rares auxquelles les membres de la filière ont contribué, classées par groupes de pathologies (depuis juillet 2021).

Hypertension pulmonaire (HTP) 02/08/23
Screening for pulmonary arterial hypertension in adults carrying a BMPR2 mutation

Montani D, Girerd B, Jaïs X, Laveneziana P, Lau EMT, Bouchachi A, Hascoët S, Günther S, Godinas L, Parent F, Guignabert C, Beurnier A, Chemla D, Hervé P, Eyries M, Soubrier F, Simonneau G, Sitbon O, Savale L, Humbert M.

Eur Respir J. 2021 Jul 22;58(1):2004229. Doi: 10.1183/13993003.04229-2020.
Hypertension pulmonaire (HTP) 02/08/23
Phenotypic Diversity of Vascular Smooth Muscle Cells in Pulmonary Arterial Hypertension: Implications for Therapy

Lechartier B, Berrebeh N, Huertas A, Humbert M, Guignabert C, Tu L.

Chest. 2021 Aug 12: S0012-3692(21)03667-9. Doi: 10.1016/j.chest.2021.08.040.
Hypertension pulmonaire (HTP) 02/08/23
Regulation of the Methylation and Expression Levels of the BMPR2 Gene by SIN3a as a Novel Therapeutic Mechanism in Pulmonary Arterial Hypertension

Bisserier M, Mathiyalagan P, Zhang S, Elmastour F, Dorfmüller P, Humbert M, David G, Tarzami S, Weber T, Perros F, Sassi Y, Sahoo S, Hadri L.

Circulation. 2021 Jul 6;144(1):52-73. Doi: 10.1161/CIRCULATIONAHA.120.047978.
Hypertension pulmonaire (HTP) 02/08/23
Pulmonary hypertension associated with neurofibromatosis type 2

Taniguchi H, Takashima T, Tu L, Thuillet R, Furukawa A, Furukawa Y, Kawamura A, Humbert M, Guignabert C, Tamura Y.

Pulm Circ. 2021 Jul 5;11(3):20458940211029550. Doi: 10.1177/20458940211029550.
Hypertension pulmonaire (HTP) 02/08/23
Lung and heart-lung transplantation for children with PAH: Dramatic benefits from the implementation of a high-priority allocation program in France

Le Pavec J, Feuillet S, Mercier O, Pauline P, Dauriat G, Crutu A, Florea V, Savale L, Levy M, Laverdure F, Stephan F, Fabre D, Delphine M, Boulate D, Mussot S, Hascoët S, Bonnet D, Humbert M, Fadel E.

J Heart Lung Transplant. 2021 Jul;40(7):652-661. Doi: 10.1016/j.healun.2021.03.013.
Hypertension pulmonaire (HTP) 02/08/23
Right Ventricle Remodeling Metabolic Signature in Experimental Pulmonary Hypertension Models of Chronic Hypoxia and Monocrotaline Exposure

Hautbergue T, Antigny F, Boët A, Haddad F, Masson B, Lambert M, Delaporte A, Menager JB, Savale L, Pavec JL, Fadel E, Humbert M, Junot C, Fenaille F, Colsch B, Mercier O.

Cells. 2021 Jun 21;10(6):1559. Doi: 10.3390/cells10061559.
Hypertension pulmonaire (HTP) 02/08/23
ERS statement on chronic thromboembolic pulmonary hypertension

Delcroix M, Torbicki A, Gopalan D, Sitbon O, Klok FA, Lang I, Jenkins D, Kim NH, Humbert M, Jais X, Vonk Noordegraaf A, Pepke-Zaba J, Brénot P, Dorfmuller P, Fadel E, Ghofrani HA, Hoeper MM, Jansa P, Madani M, Matsubara H, Ogo T, Grünig E, D’Armini A, Galie N, Meyer B, Corkery P, Meszaros G, Mayer E, Simonneau G.

Eur Respir J. 2021 Jun 17;57(6):2002828. Doi: 10.1183/13993003.02828-2020.
Hypertension pulmonaire (HTP) 02/08/23
Different cardiovascular and pulmonary phenotypes for single- and double-knock-out mice deficient in BMP9 and BMP10

Bouvard C, Tu L, Rossi M, Desroches-Castan A, Berrebeh N, Helfer E, Roelants C, Liu H, Ouarne M, Chaumontel N, Mallet C, Battail C, Bikfalvi A, Humbert M, Savale L, Daubon T, Perret P, Tillet E, Guignabert C, Bailly S.

Cardiovasc Res. 2021 Jun 4: cvab187. Doi: 10.1093/cvr/cvab187.
Hypertension pulmonaire (HTP) 02/08/23
The isobaric pulmonary arterial compliance in pulmonary hypertension

Chemla D, Berthelot E, Weatherald J, Lau EMT, Savale L, Beurnier A, Montani D, Sitbon O, Attal P, Boulate D, Assayag P, Humbert M, Hervé P.

ERJ Open Res. 2021 May 31;7(2):00941-2020. Doi: 10.1183/23120541.00941-2020.
Hypertension pulmonaire (HTP) 02/08/23
Involvement of CFTR in the pathogenesis of pulmonary arterial hypertension

Le Ribeuz H, To L, Ghigna MR, Martin C, Nagaraj C, Dreano E, Rucker-Martin C, Girerd B, Bouliguan J, Pechoux C, Lambert M, Boet A, Issard J, Mercier O, Hoetzenecker K, Manoury B, Becq F, Burgel PR, Cottart CH, Olschewski A, Sermet-Gaudelus I, Perros F, Humbert M, Montani D, Antigny F.

Eur Respir J. 2021 May 28:2000653. Doi: 10.1183/13993003.00653-2020.

FILTRER :

Par mot clé

Par maladies

Réinitialiser les filtres

Screening for pulmonary arterial hypertension in adults carrying a BMPR2 mutation

Phenotypic Diversity of Vascular Smooth Muscle Cells in Pulmonary Arterial Hypertension: Implications for Therapy

Regulation of the Methylation and Expression Levels of the BMPR2 Gene by SIN3a as a Novel Therapeutic Mechanism in Pulmonary Arterial Hypertension

Pulmonary hypertension associated with neurofibromatosis type 2

Lung and heart-lung transplantation for children with PAH: Dramatic benefits from the implementation of a high-priority allocation program in France

Right Ventricle Remodeling Metabolic Signature in Experimental Pulmonary Hypertension Models of Chronic Hypoxia and Monocrotaline Exposure

ERS statement on chronic thromboembolic pulmonary hypertension

Different cardiovascular and pulmonary phenotypes for single- and double-knock-out mice deficient in BMP9 and BMP10

The isobaric pulmonary arterial compliance in pulmonary hypertension

Involvement of CFTR in the pathogenesis of pulmonary arterial hypertension