Publications scientifiques
Voici les publications scientifiques relatives aux maladies respiratoires rares auxquelles les membres de la filière ont contribué, classées par groupes de pathologies (depuis juillet 2021).
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Pneumopathies interstitielles diffuses (PID)
Epidemiology of Childhood Interstitial Lung Disease in France: The RespiRare Cohort
Thorax 79, nᵒ 9 (août 2024): 842‑52.
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Pneumopathies interstitielles diffuses (PID)
Similarities and Differences of Interstitial Lung Disease Associated with Pathogenic Variants in SFTPC and ABCA3 in Adults
Respirology (Carlton, Vic.) 29, nᵒ 4 (avril 2024): 312‑23
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Fibrose pulmonaire - FPI
Continued Treatment with Nintedanib in Patients with Progressive Pulmonary Fibrosis: Data from INBUILD-ON
Lung 203, nᵒ 1 (janvier 2025): 25.
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Fibrose pulmonaire - FPI
Identification of progressive pulmonary fibrosis: consensus findings from a modified Delphi study
Respiratory Research 25, nᵒ 1 (décembre 2024): 448.
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Fibrose pulmonaire - FPI
Quantitative Imaging Methods in Combined Pulmonary Fibrosis and Emphysema
CHEST 166, nᵒ 6 (décembre 2024): 1463‑72
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Fibrose pulmonaire - FPI
Pulmonary fibrosis is uncommon in primary Sjögren disease
Diagnostic and Interventional Imaging 105, nᵒ 5 (mai 2024): 163‑64.
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Fibrose pulmonaire - FPI
CD206+ Macrophages Are Relevant Non-Invasive Imaging Biomarkers and Therapeutic Targets in Experimental Lung Fibrosis
Thorax 79, nᵒ 12 (novembre 2024): 1124‑35.
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Fibrose pulmonaire - FPI
Phase 2, Double-Blind, Placebo-controlled Trial of a c-Jun N-Terminal Kinase Inhibitor in Idiopathic Pulmonary Fibrosis
American Journal of Respiratory and Critical Care Medicine 210, nᵒ 4 (août 2024): 435‑43.
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Fibrose pulmonaire - FPI
Circulating Biomarkers and Progression of Idiopathic Pulmonary Fibrosis: Data from the INMARK Trial
ERJ Open Research 10, nᵒ 4 (juillet 2024): 00335‑02023
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Fibrose pulmonaire - FPI
Forced Vital Capacity Reduction Severity in Pulmonary Fibrosis and Post-Lung Transplantation Outcomes
Respiratory Medicine and Research 87 (janvier 2025): 101158