Veuillez trouver ci-dessous les publications scientifiques, recensées par la filière, en lien avec les maladies respiratoires rares, classées par groupe de pathologies.
Thoracoscopic surgery for congenital lung malformations: Does previous infection really matter?
Elhattab A, Elsaied A, Wafa T, Jugie M, Delacourt C, Sarnacki S, Aly K, Khen-Dunlop N.
J Pediatr Surg. 2021 Nov;56(11):1982-1987.
Predicting the risk of respiratory distress in newborns with congenital pulmonary malformations
Delacourt C, Bertille N, Salomon LJ, Rashenas M, Benachi A, Bonnard A, Choupeaux L, Fouquet V, Goua V, Hameury F, Hervieux E, Jouannic JM, Khen-Dunlop N, Le Bouar G, Massardier J, Roditis L, Rosenblatt J, Sartor A, Thong-Vanh C, Lelong N, Khoshnood B; MALFPULM study group.
Eur Respir J. 2021 Jul 15:2100949.
Thoracoscopic surgery for congenital lung malformations : Does previous infection really matter ?
Elhattab A, Elsaied A, Wafa T, Jugie M, Delacourt C, Sarnacki S, Aly K, Khen-Dunlop N.
J Pediatr Surg. 2021 Jan 27: S0022-3468(21)00086-5.
Intravenous pulses of methylprednisolone for infants with severe bronchopulmonary dysplasia and respiratory support after 3 months of age
Billion E, Hadchouel A, Garcelon N, Delacourt C, Drummond D.
Pediatr Pulmonol. 2021 Jan;56(1):74-82.
Obstructive Apneas in a Mouse Model of Congenital Central Hypoventilation Syndrome.
Madani A, Pitollat G, Sizun E, Cardoit L, Ringot M, Bourgeois T, Ramanantsoa N, Delclaux C, Dauger S, d’Ortho MP, Thoby-Brisson M, Gallego J, Matrot B.
Am J Respir Crit Care Med. 2021 Nov 15;204(10):1200-1210.
Management of early infection with Pseudomonas aeruginosa in adults with bronchiectasis: A survey of French pulmonologist’s practices
Schlemmer F, Murris-Espin M, Douvry B, Bergeron A, Burgel PR, Andrejak C, Maitre B.
Respir Med Res. 2021 Sep 9;80:100859.
Robotic lobectomy in children with severe bronchiectasis: A worthwhile new technology
Durand M, Musleh L, Vatta F, Orofino G, Querciagrossa S, Jugie M, Bustarret O, Delacourt C, Sarnacki S, Blanc T, Khen-Dunlop N.
J Pediatr Surg. 2021 Sep;56(9):1606-1610.
European Respiratory Society guidelines for the management of children and adolescents with bronchiectasis
Chang AB, Fortescue R, Grimwood K, Alexopoulou E, Bell L, Boyd J, Bush A, Chalmers JD, Hill AT, Karadag B, Midulla F, McCallum GB, Powell Z, Snijders D, Song WJ, Tonia T, Wilson C, Zacharasiewicz A, Kantar A.
Eur Respir J. 2021 Aug 26;58(2):2002990.
Alexandru M, de Boissieu P, Benoudiba F, Moustarhfir M, Kim S, Bequignon É, Honoré I, Garcia G, Mitri-Frangieh R, Legendre M, Crestani B, Taillé C, Escudier E, Maitre B, Papon JF, Nevoux J.
J Clin Med. 2022 Aug 31;11(17):5163.
Mabrouk I, Al-Harthi N, Mani R, Montantin G, Tissier S, Lagha R, Ben Abdallah F, Hassan MM, Alhomrani M, Gaber A, Alsanie WF, Ouali H, Jambi FA, Almaghamsi TM, Alqarni NA, Alfarsi NA, Kashgari K, Al-Zahrani HJ, Al-Shamary ZA, Al-Harbi A, Amselem S, Escudier E, Legendre M.
J Hum Genet. 2022 Jul;67(7):381-386.
Legendre M, Thouvenin G, Taytard J, Baron M, Le Bourgeois M, Tamalet A, Mani R, Jouvion G, Amselem S, Escudier E, Beydon N.
Ann Am Thorac Soc. 2022 May 27.
Epaud S, Epaud R, Salaün-Penquer N, Belozertseva E, Remus N, Douvry B, Bequignon E, Coste A, Prulière-Escabasse V, Schlemmer F, Jung C, Ortala M, Maitre B, Delestrain C.
Eur Respir J. 2022 Jan 13;59(1):2102413.
Ciliary Videomicroscopy: A Long Beat from the European Respiratory Society Guidelines to the Recognition as a Confirmatory Test for Primary Ciliary Dyskinesia
Bricmont N, Alexandru M, Louis B, Papon JF, Kempeneers C.
Diagnostics (Basel). 2021 Sep 17;11(9):1700.
Etiological Work-Up for Adults with Bronchiectasis: A Predictive Diagnostic Score for Primary Ciliary Dyskinesia and Cystic Fibrosis
Schlemmer F, Hamzaoui A, Zebachi S, Le Thuaut A, Mangiapan G, Monnet I, Boudjema A, Jabot L, Housset B, Bastuji-Garin S, Bassinet L, Maitre B.
J Clin Med. 2021 Aug 6;10(16):3478.
Topological data analysis reveals genotype-phenotype relationships in primary ciliary dyskinesia
Shoemark A, Rubbo B, Legendre M, Fassad MR, Haarman EG, Best S, Bon ICM, Brandsma J, Burgel PR, Carlsson G, Carr SB, Carroll M, Edwards M, Escudier E, Honoré I, Hunt D, Jouvion G, Loebinger MR, Maitre B, Morris-Rosendahl D, Papon JF, Parsons CM, Patel MP, Thomas NS, Thouvenin G, Walker WT, Wilson R, Hogg C, Mitchison HM, Lucas JS.
Eur Respir J. 2021 Aug 5;58(2):2002359.
International BEAT-PCD consensus statement for infection prevention and control for primary ciliary dyskinesia in collaboration with ERN-LUNG PCD Core Network and patient representatives
Marthin JK, Lucas JS, Boon M, Casaulta C, Crowley S, Destouches DMS, Eber E, Escribano A, Haarman E, Hogg C, Maitre B, Marsh G, Martinu V, Moreno-Galdó A, Mussaffi H, Omran H, Pohunek P, Rindlisbacher B, Robinson P, Snijders D, Walker WT, Yiallouros P, Johansen HK, Nielsen KG.
ERJ Open Res. 2021 Aug 2;7(3):00301-2021.
Breath-holding and tidal breathing nasal NO to screen children for Primary Ciliary Dyskinesia
Beydon N, Tamalet A, Escudier E, Legendre M, Thouvenin G.
Pediatr Pulmonol. 2021 Jul;56(7):2242-2249.
Motile cilia and airway disease
Legendre M, Zaragosi LE, Mitchison HM.
Semin Cell Dev Biol. 2021 Feb;110:19-33.
Manali ED, Kannengiesser C, Borie R, Ba I, Bouros D, Markopoulou A, Antoniou K, Kolilekas L, Papaioannou AI, Tzilas V, Tzouvelekis A, Daniil Z, Fouka E, Papakosta D, Xyfteri A, Karakatsani A, Loukides S, Korbila I, Tomos IP, Konstantinidis AK, Gogali A, Steiropoulos P, Papanikolaou IC, Bazaka C, Haritou A, Vassilakopoulos T, Maniati M, Kagouridis K, Markozannes E, Bouros E, Rampiadou C, Kounti G, Trachalaki A, Dimeas I, Karampitsakos T, Lyberopoulos P, Malamadakis N, Spyropoulou S, Revy P, Lainey E, Dieudé P, Rebah K, Ménard C, Oudin C, Masson C, Plessier A, Legendre M, Nathan N, Coulomb-L’Hermine A, Clement A, Amselem S, Boileau C, Crestani B, Papiris S; Greek Group of ILD Investigators.
Respiration. 2022 Jan 25:1-13.
Cottin V, Gueguen S, Jouneau S, Nunes H, Crestani B, Bonniaud P, Wémeau-Stervinou L, Reynaud-Gaubert M, Israël-Biet D, Cadranel J, Marchand-Adam S, Quétant S, Hirschi S, Montani D, Gamez AS, Chevereau M, Dufaure-Garé I, Amselem S, Clement A; OrphaLung and RespiFil Networks.
Respiration. 2022;101(1):34-45.
Cottin V, Guéguen S, Nunes H, Jouneau S, Crestani B, Bonniaud P, Wemeau L, Israël-Biet D, Reynaud-Gaubert M, Gondouin A, Cadranel J, Marchand-Adam S, Chevereau M, Dufaure-Garé I, Amselem S, Clément A; and the RaDiCo team.
Adv Ther. 2021 Nov 10.
Idiopathic pulmonary fibrosis: Physician and patient perspectives on the pathway to care from symptom recognition to diagnosis and disease burden
Lancaster L, Bonella F, Inoue Y, Cottin V, Siddall J, Small M, Langley J.
Respirology. 2021 Oct 5. Doi: 10.1111/resp.14154.
Post hoc Analysis of Clinical Outcomes in Placebo- and Pirfenidone-Treated Patients with IPF Stratified by BMI and Weight Loss
Jouneau S, Crestani B, Thibault R, Lederlin M, Vernhet L, Yang M, Morgenthien E, Kirchgaessler KU, Cottin V.
Respiration. 2021 Oct 5:1-13.
The Aggregate Index of Systemic Inflammation (AISI): A Novel Prognostic Biomarker in Idiopathic Pulmonary Fibrosis
Zinellu A, Collu C, Nasser M, Paliogiannis P, Mellino S, Zinellu E, Traclet J, Ahmad K, Mangoni AA, Carru C, Pirina P, Fois AG, Cottin V.
J Clin Med. 2021 Sep 14;10(18):4134.
Cyclophosphamide added to glucocorticoids in acute exacerbation of idiopathic pulmonary fibrosis (EXAFIP): a randomised, double-blind, placebo-controlled, phase 3 trial
Naccache JM, Jouneau S, Didier M, Borie R, Cachanado M, Bourdin A, Reynaud-Gaubert M, Bonniaud P, Israël-Biet D, Prévot G, Hirschi S, Lebargy F, Marchand-Adam S, Bautin N, Traclet J, Gomez E, Leroy S, Gagnadoux F, Rivière F, Bergot E, Gondouin A, Blanchard E, Parrot A, Blanc FX, Chabrol A, Dominique S, Gibelin A, Tazi A, Berard L, Brillet PY, Debray MP, Rousseau A, Kerjouan M, Freynet O, Dombret MC, Gamez AS, Nieves A, Beltramo G, Pastré J, Le Borgne-Krams A, Dégot T, Launois C, Plantier L, Wémeau-Stervinou L, Cadranel J, Chenivesse C, Valeyre D, Crestani B, Cottin V, Simon T, Nunes H; EXAFIP investigators and the OrphaLung network.
Lancet Respir Med. 2021 Sep 7: S2213-2600(21)00354-4.
Impact of Gender on the Characteristics of Patients with Idiopathic Pulmonary Fibrosis Included in the RaDiCo-ILD Cohort
Cottin V, Gueguen S, Jouneau S, Nunes H, Crestani B, Bonniaud P, Wémeau-Stervinou L, Reynaud-Gaubert M, Israël-Biet D, Cadranel J, Marchand-Adam S, Quétant S, Hirschi S, Montani D, Gamez AS, Chevereau M, Dufaure-Garé I, Amselem S, Clement A; OrphaLung and RespiFil Networks.
Respiration. 2021 Sep 2:1-12.
Nintedanib in progressive interstitial lung diseases: data from the whole INBUILD trial
Flaherty KR, Wells AU, Cottin V, Devaraj A, Inoue Y, Richeldi L, Walsh SLF, Kolb M, Koschel D, Moua T, Stowasser S, Goeldner RG, Schlenker-Herceg R, Brown KK; INBUILD trial investigators.
Eur Respir J. 2021 Sep 2:2004538.
Inhibition of the Arp2/3 complex represses human lung myofibroblast differentiation and attenuates bleomycin-induced pulmonary fibrosis
Mergault C, Lisée F, Tiroille V, Magnien M, Parent C, Lenga Mabonda W, Sizaret D, Jaillet M, Crestani B, Marchand-Adam S, Plantier L.
Br J Pharmacol. 2021 Aug 28.
Air pollution and poverty: a deadly mix in idiopathic pulmonary fibrosis ?
Sesé L, Annesi-Maesano I, Cavalin C, Nunes H.
Eur Respir J. 2021 Aug 12:2101714.
Gender Differences in Idiopathic Pulmonary Fibrosis: Are Men and Women Equal ?
Sesé L, Nunes H, Cottin V, Israel-Biet D, Crestani B, Guillot-Dudoret S, Cadranel J, Wallaert B, Tazi A, Maître B, Prévot G, Marchand-Adam S, Hirschi S, Dury S, Giraud V, Gondouin A, Bonniaud P, Traclet J, Juvin K, Borie R, Carton Z, Freynet O, Gille T, Planès C, Valeyre D, Uzunhan Y.
Front Med (Lausanne). 2021 Aug 5;8:713698.
Usefulness of Body Composition CT Analysis in Patients with Idiopathic Pulmonary Fibrosis : A Pilot Study
Jalaber C, Lemerre-Poincloux J, Jouneau S, Rousseau C, Dolou B, Rouag E, Lescoat A, Luque-Paz D, Lucas C, Vernhet L, Thibault R, Lederlin M.
Acad Radiol. 2021 Aug 17: S1076-6332(21)00328-7.
Home spirometry in patients with idiopathic pulmonary fibrosis: data from the INMARK trial
Noth I, Cottin V, Chaudhuri N, Corte TJ, Johannson KA, Wijsenbeek M, Jouneau S, Michael A, Quaresma M, Rohr KB, Russell AM, Stowasser S, Maher TM; INMARK trial investigators.
Eur Respir J. 2021 Jul 8;58(1):2001518.
Low income and outcome in idiopathic pulmonary fibrosis: An association to uncover
Sesé L, Caliez J, Annesi-Maesano I, Cottin V, Pesce G, Didier M, Carton Z, Israel-Biet D, Crestani B, Dudoret SG, Cadranel J, Wallaert B, Tazi A, Maître B, Prévot G, Marchand-Adam S, Hirschi S, Dury S, Giraud V, Gondouin A, Bonniaud P, Traclet J, Juvin K, Borie R, Bernaudin JF, Valeyre D, Cavalin C, Nunes H; COFI collaborators.
Respir Med. 2021 Jul;183:106415.
Response to letter entitled: Re: Immune checkpoint blockade for patients with lung cancer and idiopathic pulmonary fibrosis
Duchemann B, Pluvy J, Crestani B, Zalcman G, Nunes H.
Eur J Cancer. 2021 Jul;151:252-253.
Prevalence, predicting factors and impact of internet use by patients with idiopathic pulmonary fibrosis: A cross-sectional observational study
Le Garrec M, Rousseau C, Thépault F, Kerjouan M, Salé A, Jouneau S.
Respir Med Res. 2021 May;79:100818.
Immune checkpoint blockade for patients with lung cancer and idiopathic pulmonary fibrosis
Duchemann B, Pluvy J, Crestani B, Zalcman G, Nunes H.
Eur J Cancer. 2021 Mar;145:179-182.
Regulation of immune cells in lung fibrosis: the reign of regnase-1 ?
Froidure A, Crestani B.
Eur Respir J. 2021 Mar 11;57(3):2004029.
Safety and efficacy of pirfenidone and nintedanib in patients with idiopathic pulmonary fibrosis and carrying a telomere-related gene mutation
Justet A, Klay D, Porcher R, Cottin V, Ahmad K, Molina Molina M, Nunes H, Reynaud-Gaubert M, Naccache JM, Manali E, Froidure A, Jouneau S, Wemeau L, Andrejak C, Gondouin A, Hirschi S, Blanchard E, Bondue B, Bonniaud P, Tromeur C, Prévot G, Marchand-Adam S, Funke-Chambour M, Gamez AS, Ba I, Papiris S, Grutters J, Crestani B, van Moorsel C, Kannengiesser C, Borie R; OrphaLung Network.
Eur Respir J. 2021 Feb 11;57(2):2003198.
IC4 : a new combined predictive index of mortality in idiopathic pulmonary fibrosis
Zinellu A, Collu C, Zinellu E, Ahmad K, Nasser M, Traclet J, Sotgiu E, Mellino S, Mangoni AA, Carru C, Pirina P, Cottin V, Fois AG.
Panminerva Med. 2021 Jan 26.
NADPH oxidase DUOX1 sustains TGF-β1 signalling and promotes lung fibrosis
Louzada RA, Corre R, Ameziane El Hassani R, Meziani L, Jaillet M, Cazes A, Crestani B, Deutsch E, Dupuy C.
Eur Respir J. 2021 Jan 14;57(1):1901949.
Gazengel P, Hascoët S, Amsallem M, Savale L, Montani D, Mercier O, Humbert M, Fadel E, Le Pavec J. Eur Respir J. 2022 Jan 20;59(1):2102388.
Lechartier B, Berrebeh N, Huertas A, Humbert M, Guignabert C, Tu L. Chest. 2022 Jan;161(1):219-231.
Kariotis S, Jammeh E, Swietlik EM, Pickworth JA, Rhodes CJ, Otero P, Wharton J, Iremonger J, Dunning MJ, Pandya D, Mascarenhas TS, Errington N, Thompson AAR, Romanoski CE, Rischard F, Garcia JGN, Yuan JX, An TS, Desai AA, Coghlan G, Lordan J, Corris PA, Howard LS, Condliffe R, Kiely DG, Church C, Pepke-Zaba J, Toshner M, Wort S, Gräf S, Morrell NW, Wilkins MR, Lawrie A, Wang D; UK National PAH Cohort Study Consortium.
Nat Commun. 2021 Dec 7;12(1):7104.
Cottin V, Bensimon L, Raguideau F, Chaize G, Hakmé A, Levy-Bachelot L, Vainchtock A, Dallongeville J, Bouvaist H, Brenot P.
PLoS One. 2021 Dec 7;16(12):e0260483.
Valentin S, Maurac A, Sitbon O, Beurnier A, Gomez E, Guillaumot A, Textoris L, Fay R, Savale L, Jaïs X, Montani D, Picard F, Mornex JF, Prevot G, Chabot F, Humbert M, Chaouat A.
Eur Respir J. 2021 Nov 4;58(5):2004066.
Masson B, Montani D, Humbert M, Capuano V, Antigny F.
Biomolecules. 2021 Nov 27;11(12):1781.
Duflot T, Tu L, Leuillier M, Messaoudi H, Groussard D, Feugray G, Azhar S, Thuillet R, Bauer F, Humbert M, Richard V, Guignabert C, Bellien J. Metabolites. 2021 Nov 17;11(11):784.
Sex and gender in pulmonary arterial hypertension.
Cheron C, McBride SA, Antigny F, Girerd B, Chouchana M, Chaumais MC, Jaïs X, Bertoletti L, Sitbon O, Weatherald J, Humbert M, Montani D.
Eur Respir Rev. 2021 Nov 8;30(162):200330.
Boucly A, Weatherald J, Savale L, de Groote P, Cottin V, Prévot G, Chaouat A, Picard F, Horeau-Langlard D, Bourdin A, Jutant EM, Beurnier A, Jevnikar M, Jaïs X, Simonneau G, Montani D, Sitbon O, Humbert M.
Eur Respir J. 2021 Nov 4:2102419.
Involvement of CFTR in the pathogenesis of pulmonary arterial hypertension.
Le Ribeuz H, To L, Ghigna MR, Martin C, Nagaraj C, Dreano E, Rucker-Martin C, Girerd B, Bouligand J, Pechoux C, Lambert M, Boet A, Issard J, Mercier O, Hoetzenecker K, Manoury B, Becq F, Burgel PR, Cottart CH, Olschewski A, Sermet-Gaudelus I, Perros F, Humbert M, Montani D, Antigny F.
Eur Respir J. 2021 Nov 25;58(5):2000653.
Valentin S, Maurac A, Sitbon O, Beurnier A, Gomez E, Guillaumot A, Textoris L, Fay R, Savale L, Jaïs X, Montani D, Picard F, Mornex JF, Prevot G, Chabot F, Humbert M, Chaouat A.
Eur Respir J. 2021 Nov 4;58(5):2004066.
Lambert M, Mendes-Ferreira P, Ghigna MR, LeRibeuz H, Adão R, Boet A, Capuano V, Rucker-Martin C, Brás-Silva C, Quarck R, Domergue V, Vachiéry JL, Humbert M, Perros F, Montani D, Antigny F. Cardiovasc Res. 2021 Nov 1;117(12):2474-2488.
Pulmonary hypertension : A rare but severe complication of common variable immunodeficiency
Thoré P, Humbert M, Montani D.
Ann Allergy Asthma Immunol. 2021 Oct;127(4):512-513.
Pulmonary hypertension : A rare but severe complication of common variable immunodeficiency
Thoré P, Humbert M, Montani D.
Ann Allergy Asthma Immunol. 2021 Oct;127(4):512-513. Doi: 10.1016/j.anai.2021.06.016.
Association between Initial Treatment Strategy and Long-Term Survival in Pulmonary Arterial Hypertension
Boucly A, Savale L, Jaïs X, Bauer F, Bergot E, Bertoletti L, Beurnier A, Bourdin A, Bouvaist H, Bulifon S, Chabanne C, Chaouat A, Cottin V, Dauphin C, Degano B, De Groote P, Favrolt N, Feng Y, Horeau-Langlard D, Jevnikar M, Jutant EM, Liang Z, Magro P, Mauran P, Moceri P, Mornex JF, Palat S, Parent F, Picard F, Pichon J, Poubeau P, Prévot G, Renard S, Reynaud-Gaubert M, Riou M, Roblot P, Sanchez O, Seferian A, Tromeur C, Weatherald J, Simonneau G, Montani D, Humbert M, Sitbon O.
Am J Respir Crit Care Med. 2021 Oct 1;204(7):842-854. Doi: 10.1164/rccm.202009-3698OC.
Pulmonary Hypertension in Patients with Common Variable Immunodeficiency
Thoré P, Jaïs X, Savale L, Dorfmuller P, Boucly A, Devilder M, Meyrignac O, Pichon J, Mankikian J, Riou M, Boiffard E, Boissin C, De Groote P, Chabanne C, Gagnadoux F, Bergeron A, Noel N, Sitbon O, Humbert M, Montani D.
J Clin Immunol. 2021 Oct;41(7):1549-1562. Doi: 10.1007/s10875-021-01064-w.
Investigating the association between ALK Receptor Tyrosine Kinase inhibitors and pulmonary arterial hypertension: a disproportionality analysis from the WHO pharmacovigilance database
Khouri C, Hlavaty A, Roustit M, Cracowski JL, Chaumais MC, Humbert M, Montani D.
Eur Respir J. 2021 Sep 29:2101576. Doi: 10.1183/13993003.01576-2021.
Mendelian randomisation and experimental medicine approaches to IL-6 as a drug target in PAH
Toshner M, Church C, Harbaum L, Rhodes C, Villar Moreschi SS, Liley J, Jones R, Arora A, Batai K, Desai AA, Coghlan JG, Gibbs JSR, Gor D, Gräf S, Harlow L, Hernandez-Sanchez J, Howard LS, Humbert M, Karnes J, Kiely DG, Kittles R, Knightbridge E, Lam B, Lutz KA, Nichols WC, Pauciulo MW, Pepke-Zaba J, Suntharalingam J, Soubrier F, Trembath RC, Schwantes-An TL, Wort SJ, Wilkins M, Gaine S, Morrell NW, Corris PA.
Eur Respir J. 2021 Sep 29:2002463. Doi: 10.1183/13993003.02463-2020.
Five-year survival after an acute episode of decompensated pulmonary arterial hypertension in the modern management era of right heart failure
Savale L, Vuillard C, Pichon J, Boucly A, Roche A, Jevnikar M, Ebstein N, Jaïs X, Le Pavec J, Montani D, Mercier O, Sitbon O, Fadel E, Humbert M.
Eur Respir J. 2021 Sep 23;58(3):2100466. Doi: 10.1183/13993003.00466-2021.
Severe pulmonary hypertension associated with chronic obstructive pulmonary disease: A prospective French multicenter cohort
Dauriat G, Reynaud-Gaubert M, Cottin V, Lamia B, Montani D, Canuet M, Boissin C, Tromeur C, Chaouat A, Degano B, Bergot E, Sanchez O, Prevot G, Sitbon O, Thabut G, Belhadi D, de Beauregard YC, Bencherif A, Humbert M, Simonneau G, Laouenan C, Mal H.
J Heart Lung Transplant. 2021 Sep;40(9):1009-1018. Doi: 10.1016/j.healun.2021.04.021.
A CELSR1 variant in a patient with pulmonary arterial hypertension
Eyries M, Girerd B, Savale L, Soubrier F, Humbert M, Montani D.
Clin Genet. 2021 Aug 25. Doi: 10.1111/cge.14046.
Combination Therapy with STAT3 Inhibitor Enhances SERCA2a-Induced BMPR2 Expression and Inhibits Pulmonary Arterial Hypertension
Bisserier M, Katz MG, Bueno-Beti C, Brojakowska A, Zhang S, Gubara S, Kohlbrenner E, Fazal S, Fargnoli A, Dorfmuller P, Humbert M, Hata A, Goukassian DA, Sassi Y, Hadri L.
Int J Mol Sci. 2021 Aug 24;22(17):9105. Doi: 10.3390/ijms22179105.
Phenotypic Diversity of Vascular Smooth Muscle Cells in Pulmonary Arterial Hypertension: Implications for Therapy
Lechartier B, Berrebeh N, Huertas A, Humbert M, Guignabert C, Tu L.
Chest. 2021 Aug 12: S0012-3692(21)03667-9. Doi: 10.1016/j.chest.2021.08.040.
Serum and pulmonary uric acid in pulmonary arterial hypertension
Savale L, Akagi S, Tu L, Cumont A, Thuillet R, Phan C, Le Vely B, Berrebeh N, Huertas A, Jaïs X, Cottin V, Chaouat A, Tromeur C, Boucly A, Jutant EM, Mercier O, Fadel E, Montani D, Sitbon O, Humbert M, Tamura Y, Guignabert C.
Eur Respir J. 2021 Aug 5;58(2):2000332. Doi: 10.1183/13993003.00332-2020.
Association between Leflunomide and Pulmonary Hypertension
Palasset TL, Chaumais MC, Weatherald J, Savale L, Jaïs X, Price LC, Khouri C, Bulifon S, Seferian A, Jevnikar M, Boucly A, Manaud G, Pancic S, Chabanne C, Ahmad K, Volpato M, Favrolt N, Guillaumot A, Horeau-Langlard D, Prévot G, Fesler P, Bertoletti L, Reynaud-Gaubert M, Lamblin N, Launay D, Simonneau G, Sitbon O, Perros F, Humbert M, Montani D.
Ann Am Thorac Soc. 2021 Aug;18(8):1306-1315. Doi: 10.1513/AnnalsATS.202008-913OC.
Screening for pulmonary arterial hypertension in adults carrying a BMPR2 mutation
Montani D, Girerd B, Jaïs X, Laveneziana P, Lau EMT, Bouchachi A, Hascoët S, Günther S, Godinas L, Parent F, Guignabert C, Beurnier A, Chemla D, Hervé P, Eyries M, Soubrier F, Simonneau G, Sitbon O, Savale L, Humbert M.
Eur Respir J. 2021 Jul 22;58(1):2004229. Doi: 10.1183/13993003.04229-2020.
Regulation of the Methylation and Expression Levels of the BMPR2 Gene by SIN3a as a Novel Therapeutic Mechanism in Pulmonary Arterial Hypertension
Bisserier M, Mathiyalagan P, Zhang S, Elmastour F, Dorfmüller P, Humbert M, David G, Tarzami S, Weber T, Perros F, Sassi Y, Sahoo S, Hadri L.
Circulation. 2021 Jul 6;144(1):52-73. Doi: 10.1161/CIRCULATIONAHA.120.047978.
Pulmonary hypertension associated with neurofibromatosis type 2
Taniguchi H, Takashima T, Tu L, Thuillet R, Furukawa A, Furukawa Y, Kawamura A, Humbert M, Guignabert C, Tamura Y.
Pulm Circ. 2021 Jul 5;11(3):20458940211029550. Doi: 10.1177/20458940211029550.
Lung and heart-lung transplantation for children with PAH: Dramatic benefits from the implementation of a high-priority allocation program in France
Le Pavec J, Feuillet S, Mercier O, Pauline P, Dauriat G, Crutu A, Florea V, Savale L, Levy M, Laverdure F, Stephan F, Fabre D, Delphine M, Boulate D, Mussot S, Hascoët S, Bonnet D, Humbert M, Fadel E.
J Heart Lung Transplant. 2021 Jul;40(7):652-661. Doi: 10.1016/j.healun.2021.03.013.
Right Ventricle Remodeling Metabolic Signature in Experimental Pulmonary Hypertension Models of Chronic Hypoxia and Monocrotaline Exposure
Hautbergue T, Antigny F, Boët A, Haddad F, Masson B, Lambert M, Delaporte A, Menager JB, Savale L, Pavec JL, Fadel E, Humbert M, Junot C, Fenaille F, Colsch B, Mercier O.
Cells. 2021 Jun 21;10(6):1559. Doi: 10.3390/cells10061559.
ERS statement on chronic thromboembolic pulmonary hypertension
Delcroix M, Torbicki A, Gopalan D, Sitbon O, Klok FA, Lang I, Jenkins D, Kim NH, Humbert M, Jais X, Vonk Noordegraaf A, Pepke-Zaba J, Brénot P, Dorfmuller P, Fadel E, Ghofrani HA, Hoeper MM, Jansa P, Madani M, Matsubara H, Ogo T, Grünig E, D’Armini A, Galie N, Meyer B, Corkery P, Meszaros G, Mayer E, Simonneau G.
Eur Respir J. 2021 Jun 17;57(6):2002828. Doi: 10.1183/13993003.02828-2020.
Different cardiovascular and pulmonary phenotypes for single- and double-knock-out mice deficient in BMP9 and BMP10
Bouvard C, Tu L, Rossi M, Desroches-Castan A, Berrebeh N, Helfer E, Roelants C, Liu H, Ouarne M, Chaumontel N, Mallet C, Battail C, Bikfalvi A, Humbert M, Savale L, Daubon T, Perret P, Tillet E, Guignabert C, Bailly S.
Cardiovasc Res. 2021 Jun 4: cvab187. Doi: 10.1093/cvr/cvab187.
The isobaric pulmonary arterial compliance in pulmonary hypertension
Chemla D, Berthelot E, Weatherald J, Lau EMT, Savale L, Beurnier A, Montani D, Sitbon O, Attal P, Boulate D, Assayag P, Humbert M, Hervé P.
ERJ Open Res. 2021 May 31;7(2):00941-2020. Doi: 10.1183/23120541.00941-2020.
Involvement of CFTR in the pathogenesis of pulmonary arterial hypertension
Le Ribeuz H, To L, Ghigna MR, Martin C, Nagaraj C, Dreano E, Rucker-Martin C, Girerd B, Bouliguan J, Pechoux C, Lambert M, Boet A, Issard J, Mercier O, Hoetzenecker K, Manoury B, Becq F, Burgel PR, Cottart CH, Olschewski A, Sermet-Gaudelus I, Perros F, Humbert M, Montani D, Antigny F.
Eur Respir J. 2021 May 28:2000653. Doi: 10.1183/13993003.00653-2020.
PH CARE COVID survey: an international patient survey on the care for pulmonary hypertension patients during the early phase of the COVID-19 pandemic
Godinas L, Iyer K, Meszaros G, Quarck R, Escribano-Subias P, Vonk Noordegraaf A, Jansa P, D’Alto M, Luknar M, Milutinov Ilic S, Belge C, Sitbon O, Reis A, Rosenkranz S, Pepke-Zaba J, Humbert M, Delcroix M.
Orphanet J Rare Dis. 2021 May 1;16(1):196. Doi: 10.1186/s13023-021-01752-1.
Inhaled Treprostinil in Group 3 Pulmonary Hypertension
Nasser M, Kolb M, Cottin V.
N Engl J Med. 2021 May 13;384(19):1869. Doi: 10.1056/NEJMc2103465.
Additive protective effects of sacubitril/valsartan and bosentan on vascular remodelling in experimental pulmonary hypertension
Chaumais MC, Djessas MRA, Thuillet R, Cumont A, Tu L, Hebert G, Gaignard P, Huertas A, Savale L, Humbert M, Guignabert C.
Cardiovasc Res. 2021 Apr 23;117(5):1391-1401. Doi: 10.1093/cvr/cvaa200.
Outcomes of patients with decreased arterial oxyhaemoglobin saturation on pulmonary arterial hypertension drugs
Valentin S, Maurac A, Sitbon O, Beurnier A, Gomez E, Guillaumot A, Textoris L, Fay R, Savale L, Jaïs X, Montani D, Picard F, Mornex JF, Prevot G, Chabot F, Humbert M, Chaouat A.
Eur Respir J. 2021 Apr 19:2004066. Doi: 10.1183/13993003.04066-2020.
Transplantation for pulmonary arterial hypertension with congenital heart disease: Impact on outcomes of the current therapeutic approach including a high-priority allocation program
Hascoët S, Pontailler M, Le Pavec J, Savale L, Mercier O, Fabre D, Mussot S, Simonneau G, Jais X, Feuillet S, Stephan F, Cohen S, Bonnet D, Humbert M, Dartevelle P, Fadel E.
Am J Transplant. 2021 Apr 12. Doi: 10.1111/ajt.16600.
Sotatercept for the Treatment of Pulmonary Arterial Hypertension
Humbert M, McLaughlin V, Gibbs JSR, Gomberg-Maitland M, Hoeper MM, Preston IR, Souza R, Waxman A, Escribano Subias P, Feldman J, Meyer G, Montani D, Olsson KM, Manimaran S, Barnes J, Linde PG, de Oliveira Pena J, Badesch DB; PULSAR Trial Investigators.
N Engl J Med. 2021 Apr 1;384(13):1204-1215. Doi: 10.1056/NEJMoa2024277.
Preoperative C-reactive protein predicts early postoperative outcomes after pulmonary endarterectomy in patients with chronic thromboembolic pulmonary hypertension
Arthur Ataam J, Amsallem M, Guihaire J, Haddad F, Lamrani L, Stephan F, Jaïs X, Humbert M, Mercier O, Fadel E.
J Thorac Cardiovasc Surg. 2021 Apr;161(4):1532-1542.e5. Doi: 10.1016/j.jtcvs.2019.11.133.
Hypoxemia during sleep and overnight rostral fluid shift in pulmonary arterial hypertension : a pilot study
Jutant EM, Montani D, Sattler C, Günther S, Sitbon O, Garcia G, Arnulf I, Humbert M, Similowski T, Redolfi S.
Pulm Circ. 2021 Mar 30;11(2):2045894021996930. Doi: 10.1177/2045894021996930.
An endothelial activin A-bone morphogenetic protein receptor type 2 link is overdriven in pulmonary hypertension
Ryanto GRT, Ikeda K, Miyagawa K, Tu L, Guignabert C, Humbert M, Fujiyama T, Yanagisawa M, Hirata KI, Emoto N.
Nat Commun. 2021 Mar 19;12(1):1720. Doi: 10.1038/s41467-021-21961-3.
Risk Stratification in Pulmonary Arterial Hypertension : Do Not Forget the Patient Perspective
Humbert M, Lau EMT
Am J Respir Crit Care Med. 2021 Mar 15;203(6):675-677. Doi: 10.1164/rccm.202012-4350ED.
Riociguat treatment in patients with chronic thromboembolic pulmonary hypertension: Final safety data from the EXPERT registry
Ghofrani HA, Gomez Sanchez MA, Humbert M, Pittrow D, Simonneau G, Gall H, Grünig E, Klose H, Halank M, Langleben D, Snijder RJ, Escribano Subias P, Mielniczuk LM, Lange TJ, Vachiéry JL, Wirtz H, Helmersen DS, Tsangaris I, Barberá JA, Pepke-Zaba J, Boonstra A, Rosenkranz S, Ulrich S, Steringer-Mascherbauer R, Delcroix M, Jansa P, Šimková I, Giannakoulas G, Klotsche J, Williams E, Meier C, Hoeper MM; NEW COLLABORATORS LIST.
Respir Med. 2021 Mar;178:106220. Doi: 10.1016/j.rmed.2020.106220.
Characteristics and Long-term Outcomes of Pulmonary Venoocclusive Disease Induced by Mitomycin C.
Certain MC, Chaumais MC, Jaïs X, Savale L, Seferian A, Parent F, Georges M, Favrolt N, Bourdin A, Boissin C, Cottin V, Traclet J, Renard S, Noel V, Picard F, Girerd B, Ghigna MR, Perros F, Sitbon O, Bonniaud P, Humbert M, Montani D.
Chest. 2021 Mar;159(3):1197-1207. Doi: 10.1016/j.chest.2020.09.238.
Reversible pulmonary hypertension associated with multivisceral Whipple’s disease
Camboulive A, Jutant EM, Savale L, Jaïs X, Sitbon O, Mussini C, Bénichou J, Lagier JC, Humbert M, Montani D.
Eur Respir J. 2021 Feb 25;57(2):2003132. Doi: 10.1183/13993003.03132-2020.
Pulmonary Vascular Resistance in Pulmonary Arterial Hypertension: La Pièce de Résistance ?
Weatherald J, Boucly A, Savale L, Jaïs X, Montani D, Humbert M, Sitbon O.
Am J Respir Crit Care Med. 2021 Feb 15;203(4):524-525. Doi: 10.1164/rccm.202009-3664LE.
Targeting transforming growth factor-β receptors in pulmonary hypertension
Guignabert C, Humbert M.
Eur Respir J. 2021 Feb 4;57(2):2002341. Doi: 10.1183/13993003.02341-2020.
Pulmonary arterial hypertension in systemic sclerosis
Lechartier B, Humbert M.
Presse Med. 2021 Feb 3;50(1):104062. Doi: 10.1016/j.lpm.2021.104062.
Hemodynamic Response to Treatment and Outcomes in Pulmonary Hypertension Associated With Interstitial Lung Disease Versus Pulmonary Arterial Hypertension in Systemic Sclerosis : Data From a Study Identifying Prognostic Factors in Pulmonary Hypertension Associated With Interstitial Lung Disease
Chauvelot L, Gamondes D, Berthiller J, Nieves A, Renard S, Catella-Chatron J, Ahmad K, Bertoletti L, Camara B, Gomez E, Launay D, Montani D, Mornex JF, Prévot G, Sanchez O, Schott AM, Subtil F, Traclet J, Turquier S, Zeghmar S, Habib G, Reynaud-Gaubert M, Humbert M, Cottin V.
Arthritis Rheumatol. 2021 Feb;73(2):295-304. Doi: 10.1002/art.41512.
Kcnk3 Dysfunction Exaggerates The Development Of Pulmonary Hypertension Induced By Left Ventricular Pressure Overload
Lambert M, Mendes-Ferreira P, Ghigna MR, LeRibeuz H, Adão R, Boet A, Capuano V, Rucker-Martin C, Brás-Silva C, Quarck R, Domergue V, Vachiéry JL, Humbert M, Perros F, Montani D, Antigny F.
Cardiovasc Res. 2021 Jan 23: cvab016. Doi: 10.1093/cvr/cvab016.
Chronic thromboembolic pulmonary hypertension and totally implantable central venous access systems
Jevnikar M, Montani D, Savale L, Seferian A, Jutant EM, Boucly A, Preda M, Weatherald J, Bulifon S, Parent F, Brenot P, Fadel E, Sitbon O, Simonneau G, Humbert M, Jaïs X.
Eur Respir J. 2021 Jan 21;57(1):2002208. Doi: 10.1183/13993003.02208-2020.
Sleep-related breathing disorders and pulmonary hypertension
Adir Y, Humbert M, Chaouat A.
Eur Respir J. 2021 Jan 5;57(1):2002258. Doi: 10.1183/13993003.02258-2020.
Riociguat treatment in patients with pulmonary arterial hypertension : Final safety data from the EXPERT registry
Hoeper MM, Gomez Sanchez MA, Humbert M, Pittrow D, Simonneau G, Gall H, Grünig E, Klose H, Halank M, Langleben D, Snijder RJ, Escribano Subias P, Mielniczuk LM, Lange TJ, Vachiéry JL, Wirtz H, Helmersen DS, Tsangaris I, Barberà JA, Pepke-Zaba J, Boonstra A, Rosenkranz S, Ulrich S, Steringer-Mascherbauer R, Delcroix M, Jansa P, Šimková I, Giannakoulas G, Klotsche J, Williams E, Meier C, Ghofrani HA; Collaborators list.
Respir Med. 2020 Dec 3;177:106241. Doi: 10.1016/j.rmed.2020.106241.
Baldi BG, Radzikowska E, Cottin V, Dilling DF, Ataya A, Ribeiro Carvalho CR, Harari S, Koslow M, Grutters JC, Inoue Y, Gupta N, Johnson SR.
Chest. 2021 Dec 20:S0012-3692(21)05166-7.
Tuberous sclerosis complex for the pulmonologist
Rebaine Y, Nasser M, Girerd B, Leroux C, Cottin V.
Eur Respir Rev. 2021 Aug 3;30(161):200348. Doi: 10.1183/16000617.0348-2020.
Combined pulmonary fibrosis and emphysema in alpha-1-antitrypsin deficiency
Le Beller A, Nasser M, Traclet J, Blanchet-Legens AS, Kannengiesser C, Mornex JF, Cottin V.
Respir Med Res. 2021 May;79:100819. Doi: 10.1016/j.resmer.2021.100819.
[Erratum to “Screening for alpha1-antitrypsin deficiency using dried blood spot: Assessment of the first 20 months” [Rev. Mal. Respir. 37 (2020) 633-43]]
Chapuis Cellier C, Narjoz C, Zerimech F, Odou MF, Joly P, Lombard C, Mornex JF, Balduyck M.
Rev Mal Respir. 2021 Jan;38(1):125-126. Doi: 10.1016/j.rmr.2020.11.011.
Nebulised liposomal-amphotericin-B as maintenance therapy in ABPA: a randomised, multicentre, trial.
Godet C, Couturaud F, Marchand-Adam S, Pison C, Gagnadoux F, Blanchard E, Taillé C, Philippe B, Hirschi S, Andréjak C, Bourdin A, Chenivesse C, Dominique S, Bassinet L, Murris-Espin M, Rivière F, Garcia G, Caillaud D, Blanc FX, Goupil F, Bergeron A, Gondouin A, Frat JP, Flament T, Camara B, Priou P, Brun AL, Laurent F, Ragot S, Cadranel J; NebuLamB* study group and GREPI network.
Eur Respir J. 2021 Nov 11:2102218.
Lukaszewicz R, Mahay G, Boyer O, Martinet J.
Allergy. 2021 Jul 12. Doi: 10.1111/all.15001.
Bui S, Dournes G, Fayon M, Bouchet S, Burgel PR, Macey J, Murris M, Delhaes L.
Rev Mal Respir. 2021 May;38(5):466-476. Doi: 10.1016/j.rmr.2021.04.004.
[Hypersensitivity Pneumonitis: An update].
Chauvin P, Kerjouan M, Jégo P, Jouneau S, Lescoat A.
Rev Med Interne. 2021 Apr 30: S0248-8663(21)00413-6. Doi: 10.1016/j.revmed.2021.03.333
[Hot tub lung: A retrospective analysis of 14 cases].
Messe R, Barrera C, Gondouin A, Dalphin JC.
Rev Mal Respir. 2021 Jan;38(1):13-21. Doi: 10.1016/j.rmr.2020.11.005.
Philippot Q, Kannengiesser C, Debray MP, Gauvain C, Ba I, Vieri M, Gondouin A, Naccache JM, Reynaud-Gaubert M, Uzunhan Y, Bondue B, Israël-Biet D, Dieudé P, Fourrage C, Lainey E, Manali E, Papiris S, Wemeau L, Hirschi S, Mal H, Nunes H, Schlemmer F, Blanchard E, Beier F, Cottin V, Crestani B, Borie R; OrphaLung Network.
Respirology. 2022 Jan 3.
Si-Mohamed SA, Nasser M, Colevray M, Nempont O, Lartaud PJ, Vlachomitrou A, Broussaud T, Ahmad K, Traclet J, Cottin V, Boussel L.
Eur Radiol. 2022 Jan 14.
Cottin V, Spagnolo P, Bonniaud P, Nolin M, Dalon F, Kirchgässler KU, Kamath TV, Van Ganse E, Belhassen M. Front Med (Lausanne). 2021 Dec 24;8:802989.
Kreuter M, Maher TM, Corte TJ, Molina-Molina M, Axmann J, Gilberg F, Kirchgaessler KU, Cottin V. Adv Ther. 2021 Dec 22.
Hadchouel A, Delacourt C.
Eur Respir J. 2021 Dec 2:2102937.
Interstitial pneumonia with autoimmune features: challenges and controversies.
Mackintosh JA, Wells AU, Cottin V, Nicholson AG, Renzoni EA.
Eur Respir Rev. 2021 Dec 22;30(162):210177.
Airway complications in lung transplant recipients with telomere-related interstitial lung disease.
Choi B, Messika J, Courtwright A, Mornex JF, Hirschi S, Roux A, Le Pavec J, Quêtant S, Froidure A, Lazor R, Reynaud-Gaubert M, Borgne AL, Houlbracq MP, Goldberg H, El-Chemaly S, Borie R; French Group of Lung Transplantation.
Clin Transplant. 2021 Dec 1:e14552.
Phillips-Houlbracq M, Mal H, Cottin V, Gauvain C, Beier F, Sicre de Fontbrune F, Sidali S, Mornex JF, Hirschi S, Roux A, Weisenburger G, Roussel A, Wémeau-Stervinou L, Le Pavec J, Pison C, Marchand Adam S, Froidure A, Lazor R, Naccache JM, Jouneau S, Nunes H, Reynaud-Gaubert M, Le Borgne A, Boutboul D, Ba I, Boileau C, Crestani B, Kannengiesser C, Borie R; OrphaLung network.
Am J Transplant. 2021 Dec 1.
Gille T, Laveneziana P.
Eur Respir Rev. 2021 Nov 30;30(162):200355.
RaDiCo, the French national research program on rare disease cohorts.
Amselem S, Gueguen S, Weinbach J, Clement A, Landais P; RaDiCo Program.
Orphanet J Rare Dis. 2021 Oct 29;16(1):454.
Juge PA, Solomon JJ, van Moorsel CHM, Garofoli R, Lee JS, Louis-Sydney F, Rojas-Serrano J, González-Pérez MI, Mejia M, Buendia-Roldán I, Falfán-Valencia R, Ambrocio-Ortiz E, Manali E, Papiris SA, Karageorgas T, Boumpas D, Antoniou KM, Sidiropoulos P, Trachalaki A, van der Vis JJ, Jamnitski A, Grutters JC, Kannengiesser C, Borie R, Kawano-Dourado L, Wemeau-Stervinou L, Flipo RM, Nunes H, Uzunhan Y, Valeyre D, Saidenberg-Kermanac’h N, Boissier MC, Richez C, Schaeverbeke T, Doyle T, Wolters PJ, Debray MP, Boileau C, Porcher R, Schwartz DA, Crestani B, Dieudé P. Semin Arthritis Rheum.
2021 Oct;51(5):996-1004. Doi: 10.1016/j.semarthrit.2021.07.002.
Variability in Global Prevalence of Interstitial Lung Disease.
Kaul B, Cottin V, Collard HR, Valenzuela C.
Front Med (Lausanne). 2021 Nov 4;8:751181.
Nintedanib in idiopathic and secondary pleuroparenchymal fibroelastosis.
Nasser M, Si-Mohamed S, Turquier S, Traclet J, Ahmad K, Philit F, Bonniaud P, Chalabreysse L, Thivolet-Béjui F,Cottin V.
Orphanet J Rare Dis. 2021 Oct 9;16(1):419.
Diagnosis yield and safety of surgical biopsy in interstitial lung diseases: a prospective study.
Radu D, Freynet O, Kambouchner M, Boubaya M, Nunes H, Uzunhan Y, Brillet PY, Guiraudet P, Noorah MZ, Israël-Biet D, Le Pimpec-Barthes F, Juvin K, Charpentier A, Gibault L, Assouad J, Naccache JM, Antoine M, Tavolaro S, Alifano M, Honoré I, L’Huillier JP, Debrosse D, Dupin C, Pradère P, Debray MP, Cazes A, Mordant P, Castier Y, Beloucif S, Crestani B, Lévy V, Martinod E, Valeyre D.
Ann Thorac Surg. 2021 Sep 29: S0003-4975(21)01672-6. Doi: 10.1016/j.athoracsur.2021.08.056.
Hadchouel A, Drummond D, Pontoizeau C, Aoust L, Hurtado Nedelec MM, El Benna J, Gachelin E, Perisson C, Vigier C, Schiff M, Lacaille F, Molina TJ, Berteloot L, Renolleau S, Ottolenghi C, Tréluyer JM, de Blic J, Delacourt C.
Eur Respir J. 2021 Sep 9:2101554. Doi: 10.1183/13993003.01554-2021.
Tanguy J, Goirand F, Bouchard A, Frenay J, Moreau M, Mothes C, Oudot A, Helbling A, Guillemin M, Bonniaud P, Cochet A, Collin B, Bellaye PS.
Eur J Nucl Med Mol Imaging. 2021 Sep;48(10):3058-3074. Doi: 10.1007/s00259-021-05209-2.
A call for evidence in connective tissue diseases-associated interstitial lung disease.
Cottin V, Lega JC, Coury F, Nasser M.
Joint Bone Spine. 2021 Sep 15;89(1):105274. Doi: 10.1016/j.jbspin.2021.105274.
Early diagnosis of fibrotic interstitial lung disease: challenges and opportunities.
Spagnolo P, Ryerson CJ, Putman R, Oldham J, Salisbury M, Sverzellati N, Valenzuela C, Guler S, Jones S, Wijsenbeek M, Cottin V.
Lancet Respir Med. 2021 Sep;9(9):1065-1076. Doi: 10.1016/S2213-2600(21)00017-5.
The progressive fibrotic phenotype in current clinical practice.
Wells AU, Brown KK, Cottin V.
Curr Opin Pulm Med. 2021 Sep 1;27(5):368-373. Doi: 10.1097/MCP.0000000000000805.
Cottin V, Larrieu S, Boussel L, Si-Mohamed S, Bazin F, Marque S, Massol J, Thivolet-Bejui F, Chalabreysse L, Maucort-Boulch D, Jouneau S, Hachulla E, Chollet J, Nasser M.
Front Med (Lausanne). 2021 Aug 30;8:699532. Doi: 10.3389/fmed.2021.699532.
Clinical Impact of Surgical Lung Biopsy for Interstitial Lung Disease in a Reference Center.
Le Guen P, Iquille J, Debray MP, Guyard A, Roussel A, Borie R, Dombret MC, Dupin C, Ghanem M, Taille C, Khalil A, Castier Y, Cazes A, Crestani B, Mordant P.
Ann Thorac Surg. 2021 Aug 14: S0003-4975(21)01428-4. Doi: 10.1016/j.athoracsur.2021.07.038.
Tanguy J, Pommerolle L, Garrido C, Kolb M, Bonniaud P, Goirand F, Bellaye PS.
Int J Mol Sci. 2021 Aug 27;22(17):9316. Doi: 10.3390/ijms22179316.
Wijsenbeek MS, Bendstrup E, Valenzuela C, Henry MT, Moor CC, Jouneau S, Fois AG, Moran-Mendoza O, Anees S, Mirt M, Bengus M, Gilberg F, Kirchgaessler KU, Vancheri C.
Adv Ther. 2021 Jul;38(7):4040-4056. Doi: 10.1007/s12325-021-01790-y.
Kalluri M, Luppi F, Vancheri A, Vancheri C, Balestro E, Varone F, Mogulkoc N, Cacopardo G, Bargagli E, Renzoni E, Torrisi S, Calvello M, Libra A, Pavone M, Bonella F, Cottin V, Valenzuela C, Wijsenbeek M, Bendstrup E; 3rd International Summit for ILD (ISILD), Erice collaborators listed below.
Eur Respir Rev. 2021 May 25;30(160):210026. Doi: 10.1183/16000617.0026-2021.
Care Delivery Models and Interstitial Lung Disease: The Role of the Specialized Center.
Fisher JH, Cottin V.
Clin Chest Med. 2021 Jun;42(2):347-355. Doi: 10.1016/j.ccm.2021.03.013.
Nathan SD, Cottin V, Behr J, Hoeper MM, Martinez FJ, Corte TJ, Keogh AM, Leuchte H, Mogulkoc N, Ulrich S, Wuyts WA, Yao Z, Ley-Zaporozhan J, Müller-Lisse UG, Scholle FD, Brüggenwerth G, Busse D, Nikkho S, Wells AU.
J Heart Lung Transplant. 2021 Jun;40(6):494-503. Doi: 10.1016/j.healun.2021.02.006.
Nasser M, Larrieu S, Boussel L, Si-Mohamed S, Bazin F, Marque S, Massol J, Thivolet-Bejui F, Chalabreysse L, Maucort-Boulch D, Hachulla E, Jouneau S, Le Lay K, Cottin V.
Respir Res. 2021 May 24;22(1):162. Doi: 10.1186/s12931-021-01749-1.
Delestrain C, Aissat A, Simon S, Tarze A, Duprat E, Nattes E, Costes B, Delattre V, Finet S, Fanen P, Epaud R.
Br J Clin Pharmacol. 2021 May;87(5):2361-2373. Doi: 10.1111/bcp.14645.
Impact of the COVID-19 lockdown on patients suffering from idiopathic interstitial pneumonia.
Beltramo G, Cransac A, Favrolt N, Spanjaard M, Zeller M, Cottin Y, Boulin M, Bonniaud P.
Respir Med Res. 2021 May;79:100808. Doi: 10.1016/j.resmer.2020.100808.
Sleep in children and young adults with interstitial and diffuse lung disease.
Abdel-Latif Thomasson D, Abou Taam R, Berteloot L, Khirani S, Griffon L, Hadchouel A, Delacourt C, Fauroux B.
Sleep Med. 2021 Apr;80:23-29. Doi: 10.1016/j.sleep.2021.01.020.
Nintedanib and immunomodulatory therapies in progressive fibrosing interstitial lung diseases.
Cottin V, Richeldi L, Rosas I, Otaola M, Song JW, Tomassetti S, Wijsenbeek M, Schmitz M, Coeck C, Stowasser S, Schlenker-Herceg R, Kolb M; INBUILD Trial Investigators.
Respir Res. 2021 Mar 16;22(1):84. doi: 10.1186/s12931-021-01668-1.
Progressive fibrosing interstitial lung disease: a clinical cohort (the PROGRESS study).
Nasser M, Larrieu S, Si-Mohamed S, Ahmad K, Boussel L, Brevet M, Chalabreysse L, Fabre C, Marque S, Revel D, Thivolet-Bejui F, Traclet J, Zeghmar S, Maucort-Boulch D, Cottin V.
Eur Respir J. 2021 Feb 11;57(2):2002718. Doi: 10.1183/13993003.02718-2020.
Olson A, Hartmann N, Patnaik P, Wallace L, Schlenker-Herceg R, Nasser M, Richeldi L, Hoffmann-Vold AM, Cottin V.
Adv Ther. 2021 Feb;38(2):854-867. Doi: 10.1007/s12325-020-01578-6.
Legendre M, Butt A, Borie R, Debray MP, Bouvry D, Filhol-Blin E, Desroziers T, Nau V, Copin B, Dastot-Le Moal F, Héry M, Duquesnoy P, Allou N, Bergeron A, Bermudez J, Cazes A, Chene AL, Cottin V, Crestani B, Dalphin JC, Dombret C, Doray B, Dupin C, Giraud V, Gondouin A, Gouya L, Israël-Biet D, Kannengiesser C, Le Borgne A, Leroy S, Longchampt E, Lorillon G, Nunes H, Picard C, Reynaud-Gaubert M, Traclet J, de Vuyst P, Coulomb L’Hermine A, Clement A, Amselem S, Nathan N.
Eur Respir J. 2020 Dec 24;56(6):2002806. Doi: 10.1183/13993003.02806-2020.
Exposure to inorganic particles in paediatric sarcoidosis: the PEDIASARC study.
Nathan N, Montagne ME, Macchi O, Rosental PA, Chauveau S, Jeny F, Sesé L, Abou Taam R, Brocvielle M, Brouard J, Catinon M, Chapelon-Abric C, Cohen-Aubart F, Delacourt C, Delestrain C, Deschildre A, Dossier A, Epaud R, Haroche J, Houdouin V, Israel-Biet D, Juvin K, Le Jeune S, Lionnet F, Meinzer U, Mittaine M, Nunes H, Mattioni S, Naccache JM, Odièvre MH, Vincent M, Clement A, Valeyre D, Cavalin C; French Sarcoidosis Group and the Silicosis Research Group.
Thorax. 2021 Oct 21: thoraxjnl-2021-217870.
How to Tackle the Diagnosis and Treatment in the Diverse Scenarios of Extrapulmonary Sarcoidosis.
Valeyre D, Jeny F, Rotenberg C, Bouvry D, Uzunhan Y, Sève P, Nunes H, Bernaudin JF.
Adv Ther. 2021 Sep;38(9):4605-4627. Doi: 10.1007/s12325-021-01832-5.
Drug-induced sarcoidosis-like reactions.
Miedema J, Nunes H.
Curr Opin Pulm Med. 2021 Sep 1;27(5):439-447. Doi: 10.1097/MCP.0000000000000800.
Hypoxia Promotes a Mixed Inflammatory-Fibrotic Macrophages Phenotype in Active Sarcoidosis.
Jeny F, Bernaudin JF, Valeyre D, Kambouchner M, Pretolani M, Nunes H, Planès C, Besnard V.
Front Immunol. 2021 Aug 11;12:719009. Doi: 10.3389/fimmu.2021.719009.
Pacheco Y, Valeyre D, El Jammal T, Vallee M, Chevalier F, Lamartine J, Sigaudo-Roussel D, Verrier B, Israel-Biet D, Freymond N, Cottin V, Calender A.
Cells. 2021 Aug 5;10(8):1995. Doi: 10.3390/cells10081995.
Lung transplantation for sarcoidosis: outcome and prognostic factors.
Le Pavec J, Valeyre D, Gazengel P, Holm AM, Schultz HH, Perch M, Le Borgne A, Reynaud-Gaubert M, Knoop C, Godinas L, Hirschi S, Bunel V, Laporta R, Harari S, Blanchard E, Magnusson JM, Tissot A, Mornex JF, Picard C, Savale L, Bernaudin JF, Brillet PY, Nunes H, Humbert M, Fadel E, Gottlieb J.
Eur Respir J. 2021 Aug 5;58(2):2003358. Doi: 10.1183/13993003.03358-2020.
ERS clinical practice guidelines on treatment of sarcoidosis.
Baughman RP, Valeyre D, Korsten P, Mathioudakis AG, Wuyts WA, Wells A, Rottoli P, Nunes H, Lower EE, Judson MA, Israel-Biet D, Grutters JC, Drent M, Culver DA, Bonella F, Antoniou K, Martone F, Quadder B, Spitzer G, Nagavci B, Tonia T, Rigau D, Ouellette DR.
Eur Respir J. 2021 Jun 17:2004079. Doi: 10.1183/13993003.04079-2020.
Pastré J, Bouvry D, Juvin K, Benattia A, Annesi-Maesano I, Valeyre D, Nunes H, Israël-Biet D.
J Clin Med. 2021 May 5;10(9):1988. Doi: 10.3390/jcm10091988.
Lhote R, Annesi-Maesano I, Nunes H, Launay D, Borie R, Sacré K, Schleinitz N, Hamidou M, Mahevas M, Devilliers H, Bonniaud P, Lhote F, Haroche J, Rufat P, Amoura Z, Valeyre D, Cohen Aubart F.
Eur Respir J. 2021 Apr 1;57(4):2001160. Doi: 10.1183/13993003.01160-2020.